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題 名 | 異汗樣類天疱瘡--十四例病例分析=Dyshidrosiform Pemphigoid--An Analysis of 14 Cases |
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作 者 | 羅述文; 林明薇; 李定達; 劉漢南; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 21:4 2003.12[民92.12] |
頁 次 | 頁326-333 |
分類號 | 415.766 |
關鍵詞 | 異汗樣類天疱瘡; 局限型類天疱瘡; Localized pemphigoid; Dyshidrosis; |
語 文 | 中文(Chinese) |
中文摘要 | 異汗樣類天疱瘡是一種不常見的局限型類天疱瘡,以手掌及腳底出現持續性水泡的形式來表現。它的臨床表現能模仿許多其他的皮膚疾病。因此,當病患在手掌及腳底出現嚴重、常常復發的水泡,特別是在老年人而且病灶主要是以出血性的形式來表現者,異汗樣類天疱瘡這個疾病應列入考慮。正確的診斷必須靠直接免疫螢光試驗。在此,我們回顧本部自民國67年1月到民國91年4月間14位異汗樣類天疱瘡的病人,發現平均發病年齡是75歲,男女比例為10:4,最初口服類固醇控制劑量平均為每天43.57毫克,而最後類固醇的平均維持劑量是每天14.42毫克:另外將我們的病例和英文文獻中的13個病例報告做比較,可看出國內外之間,無論在發病年齡、性別、治療與預後,皆無顯著的差異存在。(中華皮誌21:326-333,2003) |
英文摘要 | Dyshidrosiform pemphigoid is an uncommon form of localized pemphigoid presenting with a persistent vesicular eruptions of the palms and soles. The clinical manifestation could mimic a variety of skin diseases. Therefore, whenever patients present with severe, recurrent blisters on their palms and soles, especially in elderly patients present with severe, recurrent blisters on their palms and soles, especially in elderly patients with hemorrhagic lesions, dyshidrosiform pemphigoid should be considered. A correct diagnosis can not be made without a positive direct immunofluorescent finding We reviewed 14 patients seen in our Department from January, 1978 to April, 2002 and found that the average age of onset is 75 years, the male-to-female ratio is 10:4, the average initial dose of oral prednisolone is 43.57 mg/day and the average maintenance dose of oral prednisolone is 14.42 mg/day. The results were then compared with those of 13 previously reported cases and revealed no significant differences in the age of onset, gender, treatment and prognosis. (Dermatol Sinica 21 : 326-333,2003) |
本系統中英文摘要資訊取自各篇刊載內容。