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來源資料
頁籤選單縮合
題 名 | Xanthomatosis Secondary to Lymphedema--Report of a Case and Review of the Literature=淋巴水腫後出現之多發性黃色瘤--病例報告及文獻回顧 |
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作 者 | 王仁暉; 曾興隆; 郭承統; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 19:2 2001.06[民90.06] |
頁 次 | 頁123-126 |
分類號 | 415.753 |
關鍵詞 | 淋巴水腫; 黃色瘤; Lymphedema; Xanthoma; Noonan syndrome; |
語 文 | 英文(English) |
中文摘要 | 一位十四歲合併有Noonan症候群的男孩,因右下肢顯著腫大,並且於腳背、踝關節及小腿等處有許多無症狀的、硬性的、肉色或黃色丘疹而來院就診。這種現象已有兩年的歷史。皮膚病理切片檢查發現在真皮層有一由許多泡沫狀組織細胞聚集而成的結節,且合併有擴大之血管、淋巴管與中性球的浸潤。相關實驗室檢查結果皆在正常範圍〈膽固醇:170mg/dl,三酸甘油脂:72mg/dl〉。一年後,病人接受整形外科手術治療淋巴水腫。手術後水腫情形逐漸改善,並且黃色丘疹數目也停止增加。本文報告此一罕見病例並回顧相關文獻。 |
英文摘要 | A 14-year-old boy of Noonan’s syndrome presented with a markedly enlarged right lower extremity and multiple asymptomatic, firm flesh-colored to yellow papules on the foot, ankle, shin and calf of 2 year’s duration. A skin biopsy specimen showed a dermal nodule of xanthomatous foamy histiocytes with dilated vessels and neutrophilic infiltrates. Dilated lymphatics were also noted, Relevant laboratory tests were within normal limits (total cholesterol: 170mg/dl, triglyceride: 72mg/dl). One year later, he received plastic surgery with Charles procedure to reduce lymphedema. Lymphedema improved gradually and xanthomatous eruption stopped to increase in number after operation. This uncommon case is reported and the literature is reviewed. |
本系統中英文摘要資訊取自各篇刊載內容。