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題 名 | Progressive Symmetric Erythrokeratodermia--A Case Report=漸進對稱性紅斑角皮症--病例報告 |
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作 者 | 甘淑鳳; 胡俊弘; 李婉若; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 21:2 2003.06[民92.06] |
頁 次 | 頁175-179 |
分類號 | 415.763 |
關鍵詞 | 漸進對稱性紅斑角皮症; 表皮增生角化; Progressive symmetric erythrokeratodermia; |
語 文 | 英文(English) |
中文摘要 | 漸進對稱性斑角皮症是一個罕見的長皮增生角化疾病,一般它屬於顯性遺傳並有不同臨床表現,但有40%的病人為偶發突變的。通常的服A酸對漸進對稱性紅斑角皮症的治療效槼良好。我們報告一個漸進對稱性紅斑角皮症病例,但此病人對口服A酸,外用類固醇、尿素、A酸及維生素D衍生物等治療,效果都不彰。 |
英文摘要 | Progressive symmetric erythrokeratodermia (PSEK) is a rare disorder disorder of cornification character- ized by epidermal hyperproliferation and is inherited as an autosomal dominant trait with variable pen- etrance. However, it has been reported that sporadic mutations comprise of 40 percent of all cases. Patients with PSEK usually respond to oral retinoid or etretinate therapy. We report a case of progress- sive symmetric erythrokeratodermia that was recalcitrant to oral acitretin and topical steroid, urea and tretinolin, as well as calcipotriol. |
本系統中英文摘要資訊取自各篇刊載內容。