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題 名 | Alternate-Sided Homonymous Hemianopia as the Solitary Presentation of Mitochondrial Encephalomyopathy, Lactic Acidosis, Stroke-Like Episodes Syndrome=以交替性同側偏盲為單獨表徵之粒腺體腦肌病伴乳酸性酸血症和中風狀發作症候群 |
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作 者 | 蘇莞雅; 高玲玉; 陳獻宗; | 書刊名 | 長庚醫學 |
卷 期 | 26:3 2003.03[民92.03] |
頁 次 | 頁199-203 |
分類號 | 416.783 |
關鍵詞 | 粒腺體腦肌病伴乳酸性酸血症和中風狀發作(EMLAS)症候群; 同側偏盲; 交替性; Mitochondrial encephalomyopathy; Lactic acidosis and stroke-like episodes (MELAS) syndrome; Homonymous hemianopia; Alternating sides; |
語 文 | 英文(English) |
中文摘要 | 粒腺體腦肌病伴乳酸性酸血症和中風狀發作(MELAS)症候群有多樣化的表現,在本篇我們報告一個以交替性同側偏盲為單獨表現的病例。一名19歲女或突發性視力模糊,併發頭痛、嘔吐、及高燒。在症狀穩定後,眼科檢查發現右側偏盲。一個月後,類偶症狀再度發生。電腦斷層攝影及核磁共振造影發現腦部左顳葉及左枕葉有便塞現象。運動測試則顯示有乳酸性酸血症(lactic acidosis)。肌肉組織檢驗則証實為粒腺體允肉病變(mitoichodrial myopathy)。半個月後病症三度發作。視野檢查發現為左側偏盲,右側視野部份恢復。而電腦斷層攝影及核磁共振造影側顯示腦部變化與視野相符。當病患有同側偏驗徵兆,合併其他反覆發作的頭痛等症狀時,必須將MELAS症候群列入考慮。 |
英文摘要 | Mitochondrial encephalomyopathy, lactic acidosis, and stroke-like episodes (MELAS) syndrome has various presentations. We report on a case of MELAS in which alternate-sided homonymous hemianopia was the main symptom of recurrent neurological defects. A 19-year-old woman suffered from blurred vision, headaches, vomiting, and facer that subsided within days. The ophthalmic examination demonstrated right homonymous hemianopia. One month later a similar episode occurred again. Computed tomography (CT) and magnetic resonance imaging (MRI) of her brain revealed an infact in the left temporo-occipital lobes. Exercise tests showed lactic acidosis, and a muscle biopsy confirmed the diagnosis of mitochnondrial myopathy. Half a monthe later, a third epsiod occurred. Visual field examination demonstrated left homonymous hemianopia and partial recovery of the right visual field. The infarct in the brain, as revealed by CT and MRI , was compatible with the visual filed changes. MELAS should be ruled out in young patients who present with homonymous hemianopia accompanied by recurrent headaches or other recurrent symptoms. |
本系統中英文摘要資訊取自各篇刊載內容。