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題 名 | Isolated Craniosynostosis: Prenatal Ultrasound of Scaphocephaly with Polyhydramnios=單純顱骨縫合過早癒合--產前超音波胎兒舟狀頭併羊水過多 |
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作 者 | 黃宣為; 林浩; 張旭陽; 許雅秀; 許德耀; | 書刊名 | 長庚醫學 |
卷 期 | 24:12 2001.12[民90.12] |
頁 次 | 頁816-819 |
分類號 | 417.343 |
關鍵詞 | 單純性的顱骨縫合過早癒合; 產前超音波; 羊水過多; 舟狀頭; Isolated craniosynostosis; Prenatal sonography; Polyhydramnios; Scaphocephaly; |
語 文 | 英文(English) |
中文摘要 | 顱骨縫合過早癒合是由於一個或數個顱縫過早癒合導致不正常暊骨形狀,包含有舟狀頭(scaphocephaly),短形頭(brachycephaly),尖頭(oxycephaly)等等。已被報告的案例中,大部份是屬於複雜或顯著的顱骨縫合過早癒合症候群,如指顱顏成骨不良,Apert氏症候群,Beare-Stevenson氏回狀皮膚症,Calabro症候群等等。而單純性顱骨縫合過早癒合在例行性超音波產前檢查中,很少被發現。我們報告一個案例是藉由產前超音波發現胎兒有長徵頭併有羊水過多的現象,無其他構造及染色體異常,且於產後以頭顱X-ray及3D立體電腦斷層來證實診斷,最後這個新生兒在三個月大時執行了頭顱憤通,直到四歲的時候發現其預後很好,就我們所知,這是文獻上的第二個案例。 |
英文摘要 | Craniosynostosis is an abnormal shape or dimension of the skill causedby premature closure of one or more skull sutures. It includes scaphocephaly, brahycephayly, oxycephal, plagiocephaly, trigonocephaly, turriecphaly, and a cloverleaf-shaped head. The only cases of craniosynostosis that have b3en reported concern fetuses with complex and marked craniosynostosis syndromes such as acrocraniofacial dysostosis, Apert’s syndrome, Beare-Stevenson cuties gyratun syndrome, Calabro’s syndrome, etc. isolated or simple craniosynostosis, however, is a developmental anomaly rarely found on routine ultrasound examination. We present case that was diagnosed as scaphocephaly with moderate ployhydramnios by prenatal ultrasound. No ohte rstructural anomal was detected, and the karyotyping was normal. So isolated asgittal craiosynostosis was diagnosed prenatally and was confirmed by postnatal skull radiography as well as 3-dimensional computed tomography. The infant underwent bilateral parietal craniectomy at the age of 3 months. He obtained a good result with no metal problems 4 years after the operation. To our knowledge, this is the second report on the prenatal detection of an isolated form of craniosynostosis. |
本系統中英文摘要資訊取自各篇刊載內容。