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題 名 | Leiomyomatosis of Mesenteric Lymph Nodes Associated with Duodenal Adenocarcinoma=十二指腸腺癌併腸繫膜淋巴腺平滑肌變化 |
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作 者 | 李錦輝; 林博彥; 張潤忠; | 書刊名 | 長庚醫學 |
卷 期 | 25:4 2002.04[民91.04] |
頁 次 | 頁271-274 |
分類號 | 416.243 |
關鍵詞 | 平滑肌變化; 腸繫膜淋巴腺; 十二指腸腺癌; Leiomyomatosis; Mesenteric lymph node; Duodenal adenocarcinoma; |
語 文 | 英文(English) |
中文摘要 | 淋巴腺之平滑肌變化是一種極為罕見的疾病,文獻中祗有幾例在骨盆淋巴腺中出現此種變化曾被報導過。這些變化過去認為和良性子宮肌肉瘤、轉移性子宮肌肉瘤、子宮內膜腺癌和卵巢之子宮內膜樣癌有關。本報告的病例是十二指腸癌的病人,在腸繫膜淋巴腺出現平滑肌變化,但之前沒有子宮平滑肌內瘤或任何婦科惡性腫瘤的病史。病人是五十六歲的女性,在十二指腸處有腺癌。所有摘除的腸繫膜淋巴腺,經由免疫螢光研究呈現平滑肌肌動蛋白陽性、硬纖維素陽性、間質纖維陽性、HMB-45陰性,顯示其具有平滑肌變化。此變化需和一些波及淋巴腺的梭狀細胞增生疾病作鑑別診斷,例如:出血性併石綿纖維之梭狀細胞腫瘤、血管肌肉脂肪瘤、淋巴血管平滑肌變化、發炎性偽瘤和卡波西氏肉瘤等。 |
英文摘要 | Leiomyomatosis of lymph nodes is an extremely rare disease. Only a few cases have previously been reported in pelvic lymph nodes. They were related to a benign uterine leiomyoma, a metastasizing uterine leiomyoma , an endometrial adencarcinoma, and an ovarian endometrioid carcinoma. We report on a case of leiomyomatosis of the mesenteric lymph nodes associated with a duodenal adenocarcinoma with no history of uterine leiomyoma or any gvnecological malignancy. The patient, a 56-year-old woman, was found to have an adenocarcinoma of the duodenum. All mesenteric lymph nodes removed showed leiomyomatosis, which was verified by immunohistochemical study showing positive immunostaining for smooth muscle actin, desmin, and vimentin, but negative staining for HMB-45. It is necessary to make a differential diagnosis from other examples of spindle cell proliferation involving lymph nodes such as a hemorrhagic spindle cell tumor with amianthoid fibers (palisade myofibroblastoma), angiomyolipoma, lymphangiomyomatosis, inflammatory pseudotumor, and Kaposi’s sarcoma. |
本系統中英文摘要資訊取自各篇刊載內容。