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題 名 | Obstructive Hypertrophic Cardiomyopathy in Taiwanese Adults=臺灣地區成年人的阻塞型肥厚性心肌病 |
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作 者 | 林俊龍; 江正文; 蕭正光; 褚柏顯; 張其任; 柯毓麟; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 98:12 1999.12[民88.12] |
頁 次 | 頁799-806 |
分類號 | 415.3165 |
關鍵詞 | 臺灣; 阻塞型肥厚性心肌病; Hypertrophic cardiomyopathy; Mortality; Prognosis; |
語 文 | 英文(English) |
英文摘要 | The purpose of this study was to analyze the clinical profiles, echocardiographic findings, and mortality among adult Taiwanese patients with obstructive hypertrophic cardiomyopathy (HCM) at Chang Gung Memorial Hospital, a university-affiliated tertiary referral center in suburban Taipei. We reviewed the medical records of all adult (>15 years of age) patients referred to our laboratory for echocardiographic examinations of cardiac diseases from May 1990 through December 1996. The diagnosis of obstructive HCM required an outflow gradient of above 10 mm Hg and the presence of asymmetric septal hypertrophy of the left ventricle. Follow-up information was obtained from hospital records, questionnaires, interviews, or the National Death Certificate Registry. Of the 6,798 adults who underwent echocardiographic examinations during the study period, 122 (1.79 % ) had obstructive HCM. The mean ± standard deviation age of the patients was 62.2 ± 12.6 years, and females predominated (n=76, 62.3%). During the mean follow-up period of 3.2 years, the annual all-cause mortality rate was 4.7%. Most deaths were due to concurrent medical conditions. The annual cardiac mortality rate was 0.99%. Logistic regression analysis identified medication with calcium channel blockers as the only negative predictor (relative risk-0.26, 95% confidence interval =0.07-0.96) of all-cause mortality, and left atrial size as the only positive predictor (relative risk=1.18, 95% confidence interval=1.02-1.37) of cardiac mortality. Cox regression analysis confirmed the former association, but not the latter. Thus, in our institution, obstructive HCM ahd a low prevalence among adult patients referred for echocardiographic examination. These patients were elderly and often had other assoicated medical conditions. The high all-cause mortality rate was largely due to non-cardiac causes. These findings suggest that obstructive HCM tends to have a benign clinical course. Large atrial size could be an independent predictor of cardiac mortality, but this possibility requires further confirmation. |
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