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頁籤選單縮合
題 名 | Extramammary Paget's Disease of the Vulva with Sclerosing Sweat Duct Carcinoma=女性陰部之乳房外柏哲氏症伴硬化性汗管癌 |
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作 者 | 吳宜珉; 曾忠仁; 邱顯清; 蕭正祥; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 19:3 2001.09[民90.09] |
頁 次 | 頁199-203 |
分類號 | 415.691 |
關鍵詞 | 陰部; 乳房外柏哲氏症; 硬化性汗管癌; Extramammary Paget's disease; Vulva; Sweat gland carcinoma; Sclerosing sweat duct carcinoma; |
語 文 | 英文(English) |
中文摘要 | 女性陰部的乳房外柏哲氏症(EMPD)是一罕見的疾病。臨床上的表現有癢感、易滲水、慢性持續存在之平的斑塊,且在女陰部有燒灼感;其組織病理學為單一或群聚、核濃染、細胞質豐富的細胞散佈於表皮內。在少數情形下,下方的汗腺癌可與女陰部EMPD合併出現。在此我們報告一65歲女性病人,其部之EMPD下方合併有硬化性汗管癌。在這個病例中,表皮內有柏哲氏細胞,而下方可見呈索狀或聚集成巢狀、核濃染之方形細胞以及一些管狀構造浸潤在硬化的真皮內。表皮的柏哲氏細胞以及浸潤性的管狀細胞染EMA和CEA都呈陽性反應。這位患者接受了廣泛性切除以及皮膚移植的治療。 |
英文摘要 | Extramammary Paget’s Disease (EMPD) of the vulva is a rare disease manifested clinically by an itching, chronically persistent patch with burning sensation on the vulva, and histopathologically by randomly scattered single or clustered cells with hyperchromatic nuclei and abundant cytoplasm in the epidermis. Rarely, an underlying sweat gland carcinoma is found accompanying vulvar EMPD. We report a case of a 65-year-old woman with EMPD of the vulva and an underlying sclerosing sweat duct carcinoma. In this case, Paget’s cells were found in the epidermis, and cords or nests of cuboidal cells with hyperchromatic nuclei and occasional ductal structures were found infiltrating the underlying sclerotic dermis. Both the Paget’s cells and the infiltrating ductal cells are positive for epithelial membrane antigen (EMA) and carcinoembryonic antigen (CEA). The patient was treated with wide excision and split-thickness skin graft. |
本系統中英文摘要資訊取自各篇刊載內容。