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題 名 | Congenital Cystic Adenomatoid Malformation of the Lung in Adults=成人之肺先天性囊狀類腺瘤異常 |
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作 者 | 程永隆; 于承平; 徐先和; 李世俊; | 書刊名 | 醫學研究 |
卷 期 | 21:4 2001.08[民90.08] |
頁 次 | 頁213-216 |
分類號 | 415.468 |
關鍵詞 | 成人; 肺; 先天性囊狀類腺瘤異常; Adult; Congenital cystic adenomatoid malformation; CCAM; Cryptorchidism; Hemopneumothorax; Lobectomy; Pneumonia; |
語 文 | 英文(English) |
英文摘要 | Congenital cystic adenomatoid malformation (CCAM) of the lung is an uncommon congenital anomaly. A majority of patients diagnosed for this condition are newborn infants, and very rarely children and adults. We report two young adults with CCAM with unusual clinical features. One is a 19-year-old man, with type I CCAM in the right upper lung, who presented with a spontaneous hemopneumothorax initially. He also had the abdominal cryptorchidism bilaterally and had received surgical treatment in his childhood. The other is a 21-year-old female with the type I CCAM at right lower lung, who had a 2-year history of recurrent pneumonia. Both patients received surgical resection of the affected lungs. They recovered uneventfully after surgery. CCAM in adults is very rate. It should be differentiated from other congenital or acquired cystic lung disorders carefully before and during surgery. Surgical resection is the standard treatment for this anomaly. |
本系統中英文摘要資訊取自各篇刊載內容。