查詢結果分析
相關文獻
- Magnetic Resonance Images of Neuronal Migration Anomalies
- 硬脊膜外麻醉導致下半身癱瘓:病例報告
- Gadolinium-Enhanced MRI in Neuro-Behcet Disease
- 擴散影像在腦缺血及梗塞診斷上的應用價值
- Lumbar Synovial Cysts: Magnetic Resonance Imaging Evaluation
- Orbital Invasion in Nasopharyngeal Carcinoma: Evaluation with Computed Tomography and Magnetic Resonance Imaging
- Primary Cardiac Tumors: Report of Two Cases
- Magnetic Resonance Imaging Features of Neuro-Behcet's Disease: A Case Report
- A Rotational Phantom for Evaluation of MR-Compatible Biopsy Devices: Experiment and Preliminary Observations
- 核黃疸病患之磁振造影表現
頁籤選單縮合
題 名 | Magnetic Resonance Images of Neuronal Migration Anomalies=神經元移行異常之磁振造影 |
---|---|
作 者 | 趙垂勳; 許瑞昇; 劉金昌; 周敏雄; | 書刊名 | The Kaohsiung Journal of Medical Sciences |
卷 期 | 14:8 1998.08[民87.08] |
頁 次 | 頁504-513 |
分類號 | 414.93 |
關鍵詞 | 神經元移行異常; 磁振造影; Neuronal migration anomalies; Brain anomalies; Magnetic resonance images; |
語 文 | 英文(English) |
中文摘要 | 在孕期第六週至五個月間的胎兒,其腦部移行中的神經母細胞,如遭受到各種原 因的傷害,即可形成一系列的腦部畸形,統稱為神經元移行異常。為了明瞭神經元移行異常 在磁振造影上的各種特徵,我們回顧了 1988 至 1996 八年間本院施行的 7116 次頭部磁振 造影檢查,共發現有 36 例神經元移行異常病例,其中 28 例為孩童,8 例為成人。分析其 磁振造影所見, 發現其中 5 例為平腦( lissencephaly ),8 例腦回平厚( pachygyria ), 12 例裂腦( schizencephaly ), 6 例灰質異位( heterotopias of gray matter ),3 例單側巨腦( hemimegalencephaly ), 2 例多小腦回( polymicrogyria )。 而 此神經元移行異常的發現率佔本院所有頭部磁振造影檢查數的 0.51 %;小兒病例則佔所有 孩童檢查數的 1.21 %。其臨床主要表徵為:抽搐( 64 %)、發展遲緩( 42 %)、運動 障礙( 42 %)及智能障礙( 25 %)。其中 25 例( 69 %)更合併有其他的腦部異常, 包括: 合併他種神經元移行異常 12 例( 33 %), 透明中隔缺少 10 例( 28 %), Dandy-Walker 畸形或變異 5 例, 蜘蛛膜囊腫 4 例, 胼胝體不發育 3 例, 全前腦( holoprosencehaly ) 2 例,巨大的小腦延髓池 1 例,及腦膨出 1 例。少數病例甚至呈現 相當複雜的多種異常。而磁振造影由於俱備優越的灰質與白質分辨能力,能清楚地顯示腦皮 質的詳細解剖構造,及擁有多重斷面的顯像效果,故可提供神經元移行異常及所合併腦部畸 形之形態變化的明確診斷。 |
英文摘要 | Neuronal migration anomalies are a spectrum of brain malformations caused by insults to migrating neuroblasts during the sixth week to fifth month of gestation. To study the characteristics of MRI findings in migration anomalies, MR images of 36 patients (28 children and 8 adults) with migration anomalies were evaluated. Five patients had lissencephaly, eight had pachygyria, twelve had schizencephaly, six had heterotopias of gray matter, three had hemimegalencephaly, and two had polymicrogyria. The frequency of migration anomalies was 0.51% of all cranial MRI studies and 1.21% of pediatric cranial MRI studies at our hospital. The major clinical presentations of these patients were seizure (64%), development delay (42%), motor deficits (42%) and mental retardation (25%). Twenty-five patients (69%) associated with other brain anomalies, including: other migration anomalies in 12 cases (33%), absence of the septum pellucidum in 10 cases (28%), Dandy-Walker malformation/variant in 5 cases, arachnoid cyst in 4 cases, agenesis of the corpus callosum in 3 cases, holoprosencephaly in 2 cases, mega cisterna magna in 1 case and cephalocele in 1 case. Some of them presented with multiple complicated anomalies. As MR imaging provides superb gray-white matter distinction, details of cortical anatomy and multiplanar capability, it can clearly delineate the detail morphologic changes of the brain caused by neuronal migration disorders as well as the associated anomalies. |
本系統中英文摘要資訊取自各篇刊載內容。