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題 名 | Adult Wilms' Tumor Associated with Polycythemia--A Case Report=成人威爾斯氏腫瘤(Wilms' Tumor)合併紅血球過多症:一病例報告 |
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作 者 | 陳啟文; 黃書彬; 李永進; 周以和; 黃俊雄; | 書刊名 | The Kaohsiung Journal of Medical Sciences |
卷 期 | 17:2 2001.02[民90.02] |
頁 次 | 頁107-111 |
分類號 | 415.818 |
關鍵詞 | 威爾斯氏腫瘤; 紅血球過多症; 腎腫瘤; Adult Wilms' tumor; Polycythemia; |
語 文 | 英文(English) |
中文摘要 | 威爾斯氏腫瘤(Wilm's tumor)在成人是罕見的,紅血球過多正在威爾斯 氏腫瘤也是罕見的表現。在此我們報告一例十分罕見的成人威爾斯氏腫瘤合併紅 血球過多症。41歲女性病人在健康檢查時超音波意外發現有右腎腫瘤。實驗室 檢查發現有紅血球過多症(血紅素20.2 g/dl)。理學檢查為正常。電腦斷層發現在 右腎中部有均勻之腫瘤,胸部X光正常。病人接受根除性右腎切除手術。切下 的腫瘤大小5×4.5×4.5 公分,周邊完整,沒有血管或集尿系統侵犯。微特徵符合 威爾斯氏腫瘤. 病人術後恢復良好,門診追蹤沒有腫瘤復發跡象。血紅素也恢復 正常(14.5 g/dl)。我們認為紅血球過多症和威爾斯氏腫瘤的關係需要小心評估, 且 手術治療是必須的。 |
英文摘要 | Both Wilms' tumor (nephroblastoma) in adults and polycythemia in Wilms' tumor are rare. Herein we report an extremely rare case of adult Wilms' tumor associated with polycythemia. A 41-year-old female was incidentally found to have right renal mass by abdominal sonography in a routine health examination. Laboratory examination revealed polycythemia (hemoglobin 20.2 g/dL). Although physical examination was unremarkable, CT scan revealed an homogeneous mass at the middle pole of right kidney, and chest x-ray revealed no metastatic lesions. Right radical nephrectomy was performed smoothly. Grossly, the tumor of 5 x 4.5 x 4.5cm in size was well circumscribed, and had no vascular structure or collecting system involvement. Microscopic features were consistent with adult nephroblastoma. The post-operative course was uneventful. At follow-up, the patient was well, showed no evidence of recurrence and her hemoglobin level had returned to normal (hemoglobin 14.5 g/dl). We suggest that the relationship between polycythemia and Wilms' tumor should be carefully evaluated before surgical treatment. |
本系統中英文摘要資訊取自各篇刊載內容。