查詢結果分析
相關文獻
- Hirschsprung's Disease Presenting with Diffuse Intestinal Pneumatosis in a Neonate
- 壞死性腸炎
- 新生兒壞死性腸炎
- Necrotizing Enterocolitis in Newborn: Nine Years' Experience
- 壞死性腸炎[Necrotizing Enterocolitis; NEC]
- 某教學醫院新生兒出生體重與頭圍之相關因素之探討
- 新生兒壞死性腸炎之外科治療
- 以緩慢增加餵食量的方式預防極低體重新生兒壞死性腸炎
- 足月產新生兒因壞死性腸炎引起大腸單一穿孔
- 伴有腸壁積氣症之嬰兒壞死性腸炎
頁籤選單縮合
題 名 | Hirschsprung's Disease Presenting with Diffuse Intestinal Pneumatosis in a Neonate=以瀰漫性腸壁積氣表現之一新生兒先天性巨結腸症 |
---|---|
作 者 | 謝武勳; 楊鵬弘; 黃振盛; 王超然; | 書刊名 | 臺灣兒科醫學會雜誌 |
卷 期 | 41:6 民89.11-12 |
頁 次 | 頁336-338+354 |
分類號 | 417.517 |
關鍵詞 | 腸壁積氣; 先天性巨結腸症; 壞死性腸炎; 短腸症候群; 新生兒; Pneumatosis intestinalis; Hirschsprung's disease; Necrotizing enterocolitis; Short bowel syndrome; Neonate; |
語 文 | 英文(English) |
中文摘要 | 新生兒時期,腹部X光檢查出理腸炎。我們報告一例女性足月新生兒,出生第二天內腹部X光即出現彌漫性腸壁內積氣,臨床上則有腹脹、含膽汁之嘔吐等疑腸陰塞的現象。腸壁內積氣在48小時內消失,但患兒經直腸壓力及下腸道顯影檢查後疑似新生兒先天性巨結腸症,經開刀及病理切片檢查後證實。術後,病人出現短腸症候群,且不幸在3個月大時死於呼吸道吸入性意外。本報告主要在提醒新生兒腹部X光出現腸壁積氣的現象時,除了懷疑可能罹患壞死性腸炎外,應該將其他造成腸陰塞之各種病因作鑑別診斷。 |
英文摘要 | In the neonate, pneumatosis intestinalis is almost always associated with necrotizing enterocolitis. The manifestation of diffuse intestinal pneumatosis in Hirschsprung's disease has been reported rarely. It may occur as a result of Hirschsprung's disease complicated with enterocolitis. We report a two-day- old female baby born at term with the problems of failure to pass meconium, progressive abdominal distension and bile stained vomiting. There was an early roentgenographic presentation of pneumatosis intestinalis which might have led to a diagnosis of necrotizing enterocolitis. However, the intestinal pneumatosis resolved within 48 hours. After anorectal manonletry and contrast enema examination, an ileostomy was performed at the age of 23 days, and multiple biopsies of intestine showed aganglionosis tip to the ileum at the level of 85cm above the ileocecal valve. Unfortunately, the patient developed short bowel syndrome after operation and died suddenly after an accidental choking at the age of three months. This case suggests that Hirschsprung's disease may have an tin usual early roentgenographic presentation with diffuse intestinal pneumatosis in the first few days of life. Anorectal manometries and suction biopsies are crucial for further diagnosis. |
本系統中英文摘要資訊取自各篇刊載內容。