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題 名 | Growth Response and Final Height in Turner Syndrome after Combination Therapy of Growth Hormone and Anabolic Steroid=透納氏病人接受生長素及同化類固醇治療後的生長反應及成人身高 |
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作 者 | 徐山靜; | 書刊名 | 臺灣兒科醫學會雜誌 |
卷 期 | 41:6 民89.11-12 |
頁 次 | 頁322-326+352 |
分類號 | 417.133 |
關鍵詞 | 透納氏症候群; 成人身高; 生長素; 同化類固醇; Turner syndrome; Final height; Growth hormone; Anabolic steroid; |
語 文 | 英文(English) |
中文摘要 | 我們給予透納氏病人生長素及同化類固醇治療,以增進她們的生長及成人身高。共33位接受過至少一年的生長素治療,劑量為1單位/公斤體重/週,每晚注射。開始治療年齡12.60±2.05歲,身高-3.2±2.1標凖誤差,年生長速度<4公分,骨齡9.9±1.7歲;第三年增加同化類固醇,劑量爲0.05毫克/公斤體重。治療中的年生長速度第一至第五年各爲:7.40;6.15;5.47;4.47;4.05公分/年。當不符健保治療條件時,即年生長速度<4公分,或骨齡超過14歲,或已達滿意身高時,需停止生長素。其中17人已達成人身高,她們平均接受生長素2.96年,同化類固醇1.86年,成人身高爲150.3±4.1公分。我們分析與療效有關的因素,幷將本研究與各國結果做一比較。我們結論以生長素及同化類固醇治療透納氏病人,可有效改進國人透納氏病人的生長及成人的身高。 |
英文摘要 | To improve the growth of Turner syndrome patients we administered human growth hormone (GH) combined with anabolic steroid. Thirty three patients completed at least one year of GH therapy. Daily GH injection was started at a dose of 1.OIU/kg/wk at age 12.6±2.1 years when their heights were below -3.2±2.1 standard deviation, growth velocity was less than 4cm/year and bone age (BA) was 9.9±1.7 years. Anabolic steroid was added at 14.3±1.3 years of age when their growth velocity slowed. Their consecutive annual growth velocities were: 7.40cm/year; 6.15cm/year; 5.47cm/year; 4.74cm/year and 4.05cm/year respectively. Growth hormone therapy was discontinued when patients grew less than 4cm/year, their BA reached 14 years or they were satisfied with their height. After combination therapy of GH for 3.0±1.1 years and anabolic steroids for 1.9±1.0 years, the final height of 17 patients was 150.3±4.Icm. We compared our results with worldwide reports and analyzed demographic factors related to growth response and final height. We conclude that combination therapy of GH and anabolic steroid is effective in improving growth and final height of Chinese Turner patients. |
本系統中英文摘要資訊取自各篇刊載內容。