查詢結果分析
來源資料
相關文獻
- Unilateral Congenital Third Cranial Nerve Palsy with Central Nervous System Anomalies: Report of Two Cases
- Treatment of Developmental Dysplasia of the Hip after Failed Open Reduction
- 先天性缺上顎側門牙的處理與探討
- 先天性頸部軟骨賸餘
- 先天性成骨不全症--脆骨症
- 先天性聽力障礙整篩檢--改革的時機
- Congenital Duodenal Membrane: A Ten-year Review
- Successful Treatment of Patent Ductus Arteriosus in Two Dogs
- Corneal Opacity and Congenital Glaucoma Associated with Massive Heparan Sulfaturia: Report of One Case
- 以治療性遊戲應用於學齡期兒童手術前的準備
頁籤選單縮合
題 名 | Unilateral Congenital Third Cranial Nerve Palsy with Central Nervous System Anomalies: Report of Two Cases=單側先天性動眼神經麻痺合併中樞神經系統畸形:二例報告 |
---|---|
作 者 | 孫啟欽; 高玲玉; | 書刊名 | 長庚醫學 |
卷 期 | 23:12 2000.12[民89.12] |
頁 次 | 頁776-781 |
分類號 | 416.7551 |
關鍵詞 | 動眼神經麻痺; 先天性; Oculomotor palsy; Congenital; |
語 文 | 英文(English) |
中文摘要 | 第三對腦神經麻痺常見於成人,且多半是由於血管病變或者壓迫性病灶所造成。然而第三對腦神經麻痺在小孩卻相當罕見且大多數是先天性的原因,與成人不同。先天性第三對腦神經麻痺過去被認為是一種良性、不合併其他神經系統異常的疾病,但是最近有許多文獻指出他們可能合併嚴重的神經系統異常或顱內畸形。本文提出兩個先天性動眼神經麻痺合併中樞神經系統畸形之病例。 第一位病患是以兩側瞳孔大小不等為表現;其他臨床表徵包括患眼的外斜視以及對側眼之下斜視,此外病患尚合併對側肢體麻痺的情形。核磁共振造影檢查發現右側中腦以及胼胝體有發育不良不全的現象。第二位病患則因出生後右眼外斜視且無光反射而來院求診,電腦斷層攝影檢查則發現腦室擴大及透明隔缺損的情形。文中除對臨床進程報告外,並對可能的致病機轉以及相關的文獻提出探討。 |
英文摘要 | The third nerve palsies are not uncommon in adults and are usually the result of vascular or compressive lesions. However, they are uncommon in children and are usually congenital. Congenital oculomotor nerve palsies were generally thought to exist in isolation without associated abnormalities: however, there have been conflicting reports in the literature as to the associations of congenital oculomotor palsies. In this report, we present 2 cases of congenital third cranial nerve palsy with neurological deficits and central nervous system abnormalities. The first patient had initial presentations of inequality in pupil size, exodeviation of the affected eye, and extreme hypotropia of the contralateral eye, which was also complicated by profound neurological deficits. Magnetic resonance imaging (MRI) scans disclosed hypoplasia of the right midbrain and corpus callosum. The second patient presented with an exodeviated right eye, and pupils non-reactive to light since birth. Computed tomography scans showed ventricular dilatation and absence of the septum pellucidum, which is compatible with septo-optic dysplasia (de Morsier syndrome). The clinical courses are presented, and we also review the literature concerning congenital third cranial nerve palsy associated with central nervous system anomalies. |
本系統中英文摘要資訊取自各篇刊載內容。