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題 名 | Adrenal Ganglioneuroma: Report of Five Cases=腎上腺神經節神經瘤:五例報告 |
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作 者 | 陳建綸; 黃世聰; 張慧朗; 吳桂芳; | 書刊名 | 長庚醫學 |
卷 期 | 23:9 2000.09[民89.09] |
頁 次 | 頁550-554 |
分類號 | 415.81 |
關鍵詞 | 腎上腺腫瘤; 神經節神經瘤; 腎上腺切除術; Adrenal tumor; Ganglioneuroma; Adrenalectomy; |
語 文 | 英文(English) |
英文摘要 | Adrenal ganglioneuromas are rare tumors originating from the neural crest tissue of the sympathetic nervous system. The clinical presentation of most patients is asymptomatic, and most of these tumors are hormone silent. Usually the tumor is detected incidentally by abdominal imaging studies for unrelated reasons. Herein, we review our cases of adrenal ganglioneuroma over the past 20 years. All patients diagnosed with primary adrenal ganglioneuroma between 1979 and 1999 were reviewed. There were 5 cases of pathologically confirmed adrenal ganglioneuroma. All patients underwent surgical excision of the adrenal tumors. The mean age of the 5 patients (3 women and 2 men) was 27 years (range, 11 to 45 years ). The average diameter of the tumor was 8.2 cm (range, 6 to 10 cm). The mean follow- up period was 33.6 months (range, 3 to 92 months). One case involved mesenteric lymph nodes. This patient had persistent hypertension following the operation, but no evidence of tumor recurrence was noted over the 7-year follow-up period. The prognosis was excellent after surgical excision in our series. Awareness of this rare entity may add to the differential diagnoses of adrenal masses preoperatively. |
本系統中英文摘要資訊取自各篇刊載內容。