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題 名 | Adult Wilms' Tumor Presenting as Acute Abdomen with Elevated Serum Lactate Dehydrogenase-4 and -5 Isoenzymes: Case Report=以急性腹痛表現以及血中乳酸鹽去氫酵素同功脢增高之成年型Wilms'腫瘤:病例報告 |
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作 者 | 莊正鏗; 吳桂芳; 廖順奎; | 書刊名 | 長庚醫學 |
卷 期 | 23:4 2000.04[民89.04] |
頁 次 | 頁235-239 |
分類號 | 415.818 |
關鍵詞 | Wilms'腫瘤; 腎胚細胞瘤; 乳酸鹽去氫酵素; 同功脢; Wilms' tumor; Nephroblastoma; Lactate dehydrogenase; Isoenzyme; |
語 文 | 英文(English) |
英文摘要 | Wilms, tumor, an embryonic neoplasm, is the most frequent renal tumor in childhood but is rare in adults. The prognosis of adult Wilms, tumor is worse than pediatric Wilms, tumor. The preoperative diagnosis of adult Wilms, tumor is extremely difficult to make because diagnostic imaging techniques, such as intravenous pyelography, computed tomography, ultrasound, renal angiography, and nuclear magnetic resonance imaging, only confirm the presence of a renal mass. Diagnosis usually depends on histological characteristics, such as the presence of blastemic, epithelial, and mesenchymal components. A 27-year-old female presented with acute abdomen and with elevated serum lactate dehydrogenase (LDH) at 212 U/l (normal range: 47 - 140), and 2 of 5 LDH isoenzymes, namely LDH-4 at 13.6% (normal range: 6.8% - 10.2%) and LDH-5 at 20% (normal range: 6.5% - 9.7%). In this patient, stage I Wilms, tumor was managed by radical nephrectomy. The levels of LDH returned to its normal range. In conclusion, in cases of acute abdomen with a renal mass in young adults, the possibility of Wilms, tumor should be considered. Serum LDH and its isoenzymes, LDH-4 and LDH-5, could be used as tumor markers for either differential diagnosis or monitoring the response of treatment. |
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