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題 名 | Situs Inversus Viscerum: Report of Two Cases=臟器反位:病例報告 |
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作 者 | 吳汐淇; 陳豐基; 王世和; 陳瑞杰; | 書刊名 | 中華民國外科醫學會雜誌 |
卷 期 | 33:2 民89.03-04 |
頁 次 | 頁72-76 |
分類號 | 415.113 |
關鍵詞 | 臟器反位; Situs inversus viscerum; |
語 文 | 英文(English) |
中文摘要 | 臟器反位是一種罕見的狀況,主要的原因係為位於第十四對染色體長臂上之反位基因的突變,造成胚胎形成時中腸部順時鐘旋轉而非逆時鐘旋轉,此狀況之發生機率約二萬分之一,以此推知,台灣地區約有一仟名患者。 本文報告二名臟器反位之病例,一為急性闌尾炎,另一則為急性膽石症合併膽管炎,病人在接受手術後皆復原良好,術後追蹤亦正常,經參考文獻及綜合整理後,在此提出經驗報告。 |
英文摘要 | Situs inversus viscerum (transposition of viscera) is a rare condition with a genetic predisposition that recessive mutation was noted in the inversus viscerum gene which was located in the long arm of chromosome 14, the incidence rate is about 1:20,000 live births. We report 2 cases with situs inversus viscerum that underwent operation, one was left sided appendicitis---who received appendectomy, the other was diagnosed cholelithiasis and choledocholithiasis-who underwent cholecystectomy and cho-ledocholithotomy and T-tube drainage. Both patients were well postopeatively and discharged uneventfully. Operation in patients of situs inversus viscerum could be safely performed, altho-ugh attentions must be paid to the details of left-right reversal. |
本系統中英文摘要資訊取自各篇刊載內容。