頁籤選單縮合
題 名 | 先天性視網膜分裂症:一病例報告及文獻回顧=Congenital Retinoschisis: A Case Report and Literature Review |
---|---|
作 者 | 洪啟庭; 陳建同; 周秉義; | 書刊名 | 國防醫學 |
卷 期 | 30:3 2000.03[民89.03] |
頁 次 | 頁238-243 |
分類號 | 416.746 |
關鍵詞 | 視網膜分裂症; 性聯遺傳性疾病; Retinoschisis; X-linked inherited disorder; |
語 文 | 中文(Chinese) |
中文摘要 | 先天性視網膜分裂症為一相當罕見之性聯遺傳性疾病,病患從幼童時期開始即有視力不佳的現象,且絕大部份終其一生均無法獲得改善。我們報告一例八歲男童從小即雙眼視力不良,一直被它院診斷為弱視,同時接受配鏡矯正治療。去年於本院眼科門診時,眼底檢查發現兩眼視網膜周邊均有分裂現象,因無立即之手術適應症,故僅建議接受門診追蹤治療。經過一年之觀察後,發現其視力與臨床徵狀並無明顯之改變。 |
英文摘要 | Congenital retinoschisis is a X-linked inherited disorder resulting in poor visual acuity. We reported a 8-year-old boy who suffered from poor vision since his child-hood. Under the impression of amblyopia at first, he received speculum correction for years. The fundus only showed peripheral retinoschisis of bilateral eyes and no immediate surgery was indicated. The clinical pictures and visual acuity remained stable after one year follow-up. The current histopathologic studies, diagnostic methods and managements were also discussed. |
本系統中英文摘要資訊取自各篇刊載內容。