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題 名 | Huge Posterior Mediastinum Liposarcoma--A Rare Case Report=巨大的後縱膈腔脂肪肉瘤--一個罕見病例報告 |
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作 者 | 黃虹綾; 李岱晃; 陳怡庭; 洪仁宇; 鍾飲文; | 書刊名 | 胸腔醫學 |
卷 期 | 30:3 2015.06[民104.06] |
頁 次 | 頁183-189 |
分類號 | 415.452 |
關鍵詞 | 縱膈腔腫瘤; 脂肪肉瘤; Mediastinal tumor; Liposarcoma; |
語 文 | 英文(English) |
中文摘要 | 我們在此報告一個病例:七十三歲女性,主訴喘及乾咳長達六個月,胸部X 光片發現疑似心包膜積水,但經胸部電腦斷層檢查後發現一巨大腫瘤位於後縱膈腔中,判斷由脂肪成分組成,手術切片檢查發現此腫瘤為一dedifferentiated liposarcoma。經手術治療後腫瘤完全緩解,並已在門診追蹤超過一年。縱膈腔之脂肪肉瘤為非常罕見之病例,目前已發表的案例報告大多數發生於前縱膈腔,此病例則發生於後縱膈腔中。此外,回顧這些文獻報告,大多數病人一開始並無明顯特異之臨床症狀,待檢查發現時之縱膈腔脂肪肉瘤大多非常巨大。手術治療是目前認為最適合之方法,大部分經過手術切除後的預後大致上都不錯,化學治療及放射線治療的角色目前並不顯著。 |
英文摘要 | We describe a 73-year-old women who presented with dyspnea and dry cough for 6 months. The chest radiograph showed a “water-bag” silhouette with widened mediastinum. The computed tomography (CT) of the chest revealed a huge posterior mediastinal mass with mixed soft tissue and fatty components, suggestive of liposarcoma. Biopsy of the lesion revealed spindle cell tumor composed of connective tissue with marked hyalinization. The patient agreed to surgery from the posterior mediastinum for complete resection. The pathological and immunohistochemical analysis confirmed the diagnosis of dedifferentiated liposarcoma. After complete resection, she had an uneventful recovery. Liposarcoma is the most common sarcoma in adults, but primary liposarcoma of the mediastinum is very rare. Mediastinal liposarcoma is often localized in the anterior mediastinum, and posterior invasion is extremely rare. The patient may present with subtle clinical symptoms until the mass reaches a giant size. Complete surgical resection remains the main treatment strategy for mediastinal liposarcoma. |
本系統中英文摘要資訊取自各篇刊載內容。