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題 名 | Langerhans' Cell Histiocytosis Involving the Eyelid of a 3-Year-Old Boy=侵犯三歲男童眼瞼的藍格罕氏組織細胞症 |
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作 者 | 陳韻如; 蕭淑卿; | 書刊名 | 中華民國眼科醫學會雜誌 |
卷 期 | 40:2 2001.06[民90.06] |
頁 次 | 頁166-168 |
分類號 | 416.752 |
關鍵詞 | 眼瞼; 藍格罕氏組織細胞症; Langerhans' cell histiocytosis; |
語 文 | 英文(English) |
中文摘要 | 本文報告一位三歲男童因反覆發作的眼瞼腫塊前來就診,經組織病理檢查,証實為藍格罕氏組織細胞症,全身檢查除了背部皮膚有相似的病灶外,並沒有發現臟器或骨骼受到侵犯,經切除眼瞼腫塊並口服類固醇,兩處病灶均痊癒,門診追蹤至今無復發。 |
英文摘要 | Langerhans' cell histiocytosis (LCH), formerly termed histiocytosis X, includes eosinophilic granuloma, Hand-Schuller-Christian disease, and Letterer-Siwe disease. All these entities are characterized by an abnormal proliferation of histiocytes. As mentioned in previous studies, it frequently involves skin, bone, lymph node and spleen. It may involve the orbit but rarely the eyelid, and may manifest as unilateral or bilateral proptosis. We report an unusual case of LCH involving the eyelids in a 3-year-old boy. |
本系統中英文摘要資訊取自各篇刊載內容。