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題 名 | Aggressive Angiomyxoma Often First Diagnosed as Bartholin Cyst: A Case Report=常被診斷為巴氏腺囊腫之侵略性血管黏液瘤:病例報告 |
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作 者 | 顧澄; 顏兆熊; 賴朝宏; | 書刊名 | 中華民國婦產科醫學會會刊雜誌 |
卷 期 | 37:3 1998.09[民87.09] |
頁 次 | 頁93-97 |
分類號 | 417.38 |
關鍵詞 | 侵略性血管黏液瘤; 巴氏腺囊腫; Aggressive angiomyxoma; Bartholin cyst; |
語 文 | 英文(English) |
中文摘要 | 背景:侵略性血管黏液瘤為一罕見之軟組織間葉腫瘤,好發於女性的骨盆與會陰 部位。自從一九八三年美國的 Steeper 與 Rosai 第一次提出九個病例報告,並首次使用了 「侵略性血管黏液瘤」的正式名稱以來,全球已有九十四例曾於英文醫學雜誌上發表。 病例報告:本病例有典型的臨床及病理表現:曾二度被診斷為巴氏腺囊腫,做廣泛局部切除 後,發現其腫瘤外觀呈現紅色、發亮;組織呈黏液樣且有彈性。病理切片可見許多增生的血 管以及梭狀、星狀的腫瘤細胞,密佈在黏液樣的基質中。此種腫瘤介於良性與惡性之間,因 它只會局部侵入,而不會轉移,也不見顯微鏡下的非典型有絲分裂;但它經常復發,且通常 此種腫瘤都相當大,故稱為「侵略性」的腫瘤。本病例於術後追蹤一年以上,且發現有復發 現象。 結論:侵略性血管黏液瘤的治療方法為廣泛局部切除,如有復發則再作切除。雖然其成功治 癒的機會相當大,但必須接受長期的追蹤檢查。 |
英文摘要 | Background: Aggressive angiomyxoma is an uncommon mesenchymal neoplasm which predominantly involves the female pelvis and perineum. Since its initial description in 1983 by Steeper and Rosai, a total of nearly 100 cases, including 6 males, have been reported in the English literature. Case Report: Our case presents with typical clinical and pathological pictures. She was first diagnosed as having a Bartholin cyst, however, a wide excision was performed under the second impression of myxoma. The excised myxoid mass was gelatinous and glistening, reddish and rubbery. lt's pathology showed numerous variable-sized blood vessels, and abundant spindle-shaped to stellate cells set in hypocellular myxoid stroma. Conclusion: This tumor was locally infiltrative, but it did not metastasize and atypical mitotic figures were absent. However, local recurrence is common, which characterizes this tumor's "aggressive" nature. The treatment of choice is wide local excision. The overall cure rate is high, but longterm follow-up is necessary. |
本系統中英文摘要資訊取自各篇刊載內容。