頁籤選單縮合
題 名 | Pulmonary Artery Leiomyosarcoma=肺動脈平滑肌肉瘤之一病例報告 |
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作 者 | 詹世鴻; 蔡良敏; 蔡惟全; 李貽恆; 陳志鴻; 羅傳堯; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 98:8 1999.08[民88.08] |
頁 次 | 頁578-581 |
分類號 | 415.384 |
關鍵詞 | 肺動脈平滑肌肉瘤; Pulmonary artery; Sarcoma; Leiomyosarcoma; |
語 文 | 英文(English) |
英文摘要 | Pulmonary artery leiomyosarcoma is a rare but highly lethal disease, and can be mistaken for pulmonary thromboembolism. We report a case of pulmonary artery leiomyosarcoma managed with surgical resection, chemotherapy, and radiotherapy. A 57-year-old woman was admitted with complaints of aggravated dyspnea. She was initially treated with oxygen therapy and heparinization for a suspected pulmonary embolism. Echocardiography revealed a dilated right atrium and ventricle and severe tricuspid regurgitation, with an estimated systolic right ventricular pressure of 95 mmHg; a shadow of a mass in the main pulmonary artery was also noted. Right ventriculography revealed a filling defect, and to-and-fro motion of the mass in the main pulmonary artery. The left pulmonary artery was almost totally occluded by the mass. The patient's condition improved dramatically after palliative excision of the mass and patch reconstruction of the outflow tract of the right ventricle with a bicuspid xenograft. Pathologic examination of the mass revealed leiomyosarcoma. Chemotherapy and radiotherapy were subsequently administered and follow-up imaging studies 3 months postoperatively revealed no recurrence of the tumor. The patient remains well, more than 1 year after treatment. This report emphasises that pulmonary artery sarcoma should be considered in the differential diagnosis in cases of suspected pulmonary thromboembolism. |
本系統中英文摘要資訊取自各篇刊載內容。