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題 名 | 局部放射治療對腦幹部位不成熟畸胎瘤之治療效果--病例報告=The Therapeutic Effect of Limited-Field Radiotherapy on Immature Teratoma of Brainstem--A Case Report |
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作 者 | 陳虹汶; 賴允亮; 張國華; 鍾昌宏; 吳孟浩; 王銘志; 陳裕仁; 黃福昭; 呂衍達; | 書刊名 | 放射治療與腫瘤學 |
卷 期 | 6:2 1999.06[民88.06] |
頁 次 | 頁149-154 |
分類號 | 416.291 |
關鍵詞 | 不成熟畸胎瘤; 放射治療; 腦幹腫瘤; 立體定位放射治療; Immature teratoma; Radiotherapy; Brainstem tumor; Stereotectic radiotherapy; |
語 文 | 中文(Chinese) |
中文摘要 | 探討一罕見腦幹部位不成熟畸胎瘤,術後經局部放射治療及立骷定位放射治療的 效果。 材料與方法:一21歲女性因吸入性肺炎入院,經檢查為腦幹腫瘤引起咽反射(gag ref1ex) 功能缺失,導致食物吸入性肺炎的反衼發生。並兩次出現突發性呼吸衰竭、血壓下降之危象。 因腫瘤位於腦幹生命中樞,腦部顯微手術僅能部份摘除。病理報告顯示為不成熟畸胎瘤( immature teratoma)。術後之化學治療因再度發生呼吸停止、血壓下降而半途中止。為維持 生命中樞的正常運作,予以局部放射治療,共39.6 Gy至計劃標的物體積。之後並以立體定 位放射治療,對局部腫瘤追加至總劑量54.6 Gy。放射治療完成後兩週開始每月一次的化學 治療,至今四次。 結果:在整個放射治療結束後,血清及腦脊液中的阿發-胎兒蛋白(alpha fetoprotein , AFP)、貝他-人類絨毛膜性腺激素(β-HCG)均由放射治療前的不正常偏高回復正常值。咽 反射的功能逐漸恢復,不需再藉鼻胃管進食,亦不再有嗆到(chocking)或吸入性肺炎的發 生。生命中樞的運作自開始放射治療起即持續穩定,不再有呼吸中止、血壓改變之危象。 結論:對腦幹部位之不成熟畸胎瘤,本文有限的經驗下顯示局部放射治療合併立體定位放 射治療對腫瘤局部控制及迅速緩解致命症狀均有正面的效果。 |
英文摘要 | Purpose: To report a rare case of brainstem immature teratoma treated by post-operative limited-field radiotherapy and stereotactic radiotherapy. Materials and Methods: A 21-year-old female presented with symptoms and signs of recurrent aspiration pneumonia that was caused by dysphagia. She had two episodes of acute respiratory arrest and hypotension while in the hospital. Computed tomography (CT) of the brain revealed a heterogenous mass at lower brain stem region. Microscopic surgery only could yielded a piece of tumor that disclosed the entity of immature teratoma. Adjuvant chemotherapy with the regimen of cisplatin, etoposide, and bleomycin was administered, but was interrupted due to sudden onset of respiratory arrest. In order to maintain brainstem function, limited-field irradiation with 39.6 Gy to planning target volume followed by a boost dose to the primary site by stereotactic radiotherapy were performed with a total dose of 54.6 Gy. Two weeks after radiotherapy, the patient began receiving monthly adjuvant chemotherapy for 4 cycles up to the time of this report. Results: Previously elevated serum and cerebrospinal fluid (CSF) levels of both alpha-fetoprotein and beta human-chorionic gonadotropin returned to a normal range after irradiation. The swallowing reflex gradually improved and the patient did not develop aspiration pneumonia again even after the NG tube was removed. Brainstem function has remained stable following irradiation. Conclusion: Our limited experience suggests that limited field radiotherapy followed by a boost dose with stereotactic radiotherapy is very effective in treating brainstem immature teratoma for both local tumor control and relief of life-threatening symptoms. |
本系統中英文摘要資訊取自各篇刊載內容。