頁籤選單縮合
題 名 | 健康孩童的鼻腦型白黴菌病--病例報告=Rhinocerebral Mucormycosis in an Otherwise Healthy Child--Case Report |
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作 者 | 陳柏年; 李國森; 王麟殿; 張克昌; | 書刊名 | 中華民國耳鼻喉科醫學雜誌 |
卷 期 | 34:5 民88.09-10 |
頁 次 | 頁403-407 |
分類號 | 415.15 |
關鍵詞 | 鼻腦型白黴菌病; 鼻-眼眶-大腦型; 健康孩童; Rhinocerebral mucormycosis; Rhino-orbito-cerebral; Amphotericin B; Healthy child; |
語 文 | 中文(Chinese) |
中文摘要 | 鼻腦型白黴菌病(rhinocerebral mucormycosis)是一種具侵襲性與高致死率的 疾病。其為少見的伺機性黴菌感染,主要發生於合併糖尿病(最常見)、免疫抑制劑治療、 癌症或其他慢性疾病的患者。然而發生於無任何潛在疾病患者則相當罕見,回顧文獻記載 僅有18例,其中2例發生於孩童。在此,我們提出1例發生於健康孩童的高致命性鼻-眼眶 -大腦型白黴菌病的病例。疾病的診斷係由鼻竇擴創術後的組織學檢查而得,術後,此病 患接受全身性amphotericin B治療。由於病例罕見,特提出報告。 |
英文摘要 | Rhinocerebral mucormycosis is a potentially aggressive and commonly fatal disease. This disease is a rare opportunistic fungal infection, occurring mainly in patients with diabetic ketoacidosis (the most common), immunosuppressive therapy, malignancy, or other chronic debilitating disorders. In other words, it was very rarely seen in an otherwise healthy individual. According to a literature review, only 18 well-documented cases without any predisposing factor have been previously reported. Two of these occurred in children. We reported a case of rhino-orbito-cerebral mucormycosis occurring in an otherwise healthy child that was successfully treated. The diagnosis was made by histologic examination of infected tissue obtained at the time of surgical debridement. Systemic amphotericin B was also given. We emphasize the importance of early diagnosis and prompt, appropriate medical and surgical therapy to achieve a significant survival rate in patients with this highly fatal disease. |
本系統中英文摘要資訊取自各篇刊載內容。