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題 名 | 聽覺神經病變--病例報告=Auditory Neuropathy--Case Report |
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作 者 | 許權振; | 書刊名 | 中華民國耳鼻喉科醫學雜誌 |
卷 期 | 34:2 民88.03-04 |
頁 次 | 頁169-172 |
分類號 | 416.865 |
關鍵詞 | 耳聲傳射檢查; 腦幹聽性反應; 聽反射; 聽覺神經病變; Otoacoustic emissions; Auditory brainstem response; Acoustic reflex; Auditory neuropathy; |
語 文 | 中文(Chinese) |
中文摘要 | 聽覺神經病變乃指介於耳蝸內毛細胞和聽覺神經元細胞間的輸入聽覺系統的病變 。本部經驗 1 名 7 歲男孩因漸進性聽覺反應不好而前來就診,兩耳聽力檢查結果:純音聽 力檢查正常,鼓室圖正常,耳聲傳射檢查正常,無聽反射,腦幹聽性反應閾值檢查(滴答聲 ,57.7/s,95 dB nHL ),兩耳均無波形出現,腦幹聽性反應的神經耳科學檢查(滴答聲, 11.1/s,85 dB nHL ),兩耳均呈 I 波延長而 III、V 波缺失。病人無中樞神經症狀,電 腦斷層攝影結果,耳蝸、聽神經和腦幹無異常。這些特性符合聽覺神經病變的診斷,在國內 尚無此類病例報告,特提出報告。 |
英文摘要 | The purpose of the present paper is to report a case of a rather exceptional form of auditory dysfunction that is characterized by abnormal auditory brainstem response (ABR) and normal distortion product otoacoustic emissions. This peculiar pattern of auditory dysfunction was recently termed" auditory neuropathy ". There is no such case reported before in Taiwan. This case is a 7 year-old boy complained of hearing impairment for 1 year. His diagnostic profile included normal pure-tone hearing, normal tympanogram, normal distortion product otoacoustic emissions, absent acoustic reflexes, and abnormal auditory brainstem response on both sides. Auditory brainstem esponse showed delayed wave I and absence of waves III and bilaterally. Using only otoacoustic emissions as a hearing screening test may result in a false-negative radeing. Therefore, ABR testing combined with otoacoustic emissions testing is recommended for children with suspicious hearing loss. |
本系統中英文摘要資訊取自各篇刊載內容。