查詢結果分析
相關文獻
- Leukocyte Adhesion Deficiency Disorder: Report of One Case
- Gallbladder Wall Thickening in a Child with Infectious Mononucleosis: Report of a Case
- 白血球沾黏分子缺乏症
- Lung Cancer with Hypercalcemia: Case Analysis and Literature Review
- The Significance of Body Temperature, C-reactive Protein and Leukocyte Count in Acute Illness in the Emergency Department
- 認識禽馬立克氏病病毒和禽白血球增多病(先天性和後天性)之研究--腦病灶、病毒增殖、細胞浸潤抗原和人工接種細菌結果
- 頭頸部癌患者之腫瘤伴生徵候群
- 可溶型內皮細胞selectin與早期頸動脈硬化
- Predictive Inflammatory Parameters in the Diagnosis of Acute Appendicitis in Children
- EB病毒引起之傳染性單核白血球增多症--78例分析
頁籤選單縮合
題 名 | Leukocyte Adhesion Deficiency Disorder: Report of One Case=白血球沾黏分子缺乏症:一病例報告 |
---|---|
作 者 | 洪志興; 錢新南; 華一鳴; 王志祿; 陳遠浩; 楊崑德; | 書刊名 | 中華民國小兒科醫學會雜誌 |
卷 期 | 40:2 民88.03-04 |
頁 次 | 頁128-131+142 |
分類號 | 417.509 |
關鍵詞 | 沾黏分子; 趨化作用; 白血球增多; Adhesion molecule; Chemotaxis; Ieukocytosis; |
語 文 | 英文(English) |
中文摘要 | 白血球沾黏分子缺乏症是一種非常罕見的疾病,至今全世界僅有數十例報告。本病例為三 十二天大女嬰,出生及家族史無特別,因臍帶延遲脫落及週圍紅腫住進本院,經抗生素治療五天後 出院,三天後症狀復發再行住院,入院時血中白血球高達86800/cumm。根據上述病史及實驗室數 據,高度懷疑她是白血球沾黏分子缺乏症的病人,經流式細胞分析儀證實病人白血球上CD11b/CD18 沾黏分子完全缺乏,證實此一病例。 |
英文摘要 | In this paper, a case of leukocyte adhesion deficiency disorder confirmed by flow cytometry and leukocyte chemotaxis assays is reported. The 32-day-old female infant was admitted to our ward on account of delayed umbilical cord detachment and omphalitis. After admission, hemogram revealed severs leukocytosis (white blood cell (WBC) counts: 86,800/cumm), and there was poor clinical response to several kinds of antibiotics. The above history indicated that the patient might be a case of leukocyte adhesion deficiency disorder. A definite absence of CD11b/CD18 adhesion molecule on the patient's granulocytes and severe defects of leukocyte function demonstrated by chemotaxis, chemokinesis and zymosan-induced respiratory burst assays confirmed this diagnosis. |
本系統中英文摘要資訊取自各篇刊載內容。