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題 名 | Atypical Central Neurocytoma: Report of a Case=非典型中樞神經細胞瘤 |
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作 者 | 周玉瑜; 李進成; 陳東榮; 魏志鵬; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 98:8 1999.08[民88.08] |
頁 次 | 頁573-577 |
分類號 | 415.83 |
關鍵詞 | 非典型中樞神經細胞瘤; Central neurocytoma; Proliferative index; Ki-67; Mitosis; Synaptophysin; Oligodendroglioma; Ependymoma; |
語 文 | 英文(English) |
英文摘要 | Central neurocytomas are rare, relatively benign intraventricular neoplasms composed of uniform round cells with neuronal differentiation. The majority of previously reported central neurocytomas did not recur after tumor removal and the patients had favorable postoperative outcomes. Only a few cases with malignant histopathology or malignant behavior have been noted. Atypical central neurocytoma is a new entity that was first described in the literature in 1997. The tumors have been noted to exhibit a Ki-67 labeling index of 2% or more, or vascular proliferation, mitoses, and necrosis, or both. Atypical histologic findings are usually associated with a somewhat less favorable clinical course and requires postoperative radiotherapy. We report a unique case of a 33-year-old man with a large intraventricular central neurocytoma. The characteristic histopathologic picture, the immunoreactivity for both synaptophysin and neuron-specific enolase, and the ultrastructural features of neuronal differentiation distinguished it from ependymoma and oligodendroglioma. The mitotic activity (up to 3 mitoses/10 high power field) and the high percentage of Ki-67-staining tumor cells (labeling index, 5.0%) in our case were consistant with the atypical variant of central neurocytoma. The patient underwent craniotomy and partial resection of the tumor. Unfortunately, he died of hydrocephalus and brain edema, the next day. |
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