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題 名 | 腸系膜脂層炎--一病例報告=Mesenteric Panniculitis--A Case Report |
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作 者 | 張介山; 劉泰成; 林錫泉; 高進祿; 李居仁; 張國明; | 書刊名 | 內科學誌 |
卷 期 | 10:1 1999.02[民88.02] |
頁 次 | 頁17-21 |
分類號 | 415.556 |
關鍵詞 | 腸系膜脂層炎; 腸系膜脂質失養症; 硬化性腸系膜炎; 縮性腸系膜炎; Mesenteric panniculitis; Mesenteric lipodystrophy; Sclerosing mesenteritis; Retractile mesenteritis; |
語 文 | 中文(Chinese) |
中文摘要 | 一位23歲女性因腹痛求診,理學檢查發現腹部腫塊,腹部超音波檢查證實腫塊的 存在。腹部電腦斷層攝影顯示一含脂肪密度之巨大腸系膜腫塊。小腸攝影檢查發現小腸被腫 塊推擠至腹腔周邊。剖腹探查與病理學檢查證實為腸系膜脂層炎。腸系膜脂層炎是一極罕見 的腸系膜發炎性疾病,此病除少數併發嚴重合併症者外,一般預後良好,自限性的病程是其 通則。雖然其確切診斷需倚靠病理學檢查,術前診斷不易,然而影像學檢查對於診斷仍有很 大的幫助。一界限清楚、混合脂肪與軟組織密度之腸系膜腫塊,腸系膜血管被包圍於其中而 不被侵犯是其典型特徵。一旦懷疑此大疾病,施行腹腔鏡術取得病灶標本以確定診斷,避免 剖腹手術和廣泛性的腸切除,是較佳的選擇。本篇探討其臨床表現、診斷、治療及預後。 。 |
英文摘要 | A 23-year-old female patient came to our hospital due to periumbilical pain. Physical examination disclosed a palpable abdominal mass. Abdominal ultrasonography proved the presence of lesion. Abdominal CT scan revealed a huge fatty mass located in the mesentery. Small bowel series showed bowel loops displacement. Laparotomy and histologic examination gave the diagnosis of mesenteric panniculitis. Mesenteric panniculitis is a very rare disease. Except for a few complicated, fatal cases, the prognosis is usually favorable. Spontaneous remission is generally the rule. Pathologic examination is still necessary for definite diagnosis. Although preoperative confirmation of the disease is difficult, imaging study can be helpful. A well-defined mesenteric mass with soft tissue and fatty components, encompassing but not invading mesenteric vessels, is the classical picture. Once the disease is suspected, laparoscopic examination for tissue proof is the option of choice. Laparotomy with extensive bowel resection is best avoided. The clinical presentation, diagnosis, treatment, and prognosis of the disease were discussed here. |
本系統中英文摘要資訊取自各篇刊載內容。