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題 名 | 神經纖維瘤病合併空腸平滑肌肉瘤及消化道出血:病例報告=Jejunal Leiomyosarcoma with Gastrointestinal Hemorrhage--An Unusal Associated Manifestation of Neurofibromatosis |
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作 者 | 李俊毅; 施壽全; 陳杉隆; | 書刊名 | 內科學誌 |
卷 期 | 10:1 1999.02[民88.02] |
頁 次 | 頁13-16 |
分類號 | 415.83 |
關鍵詞 | 神經纖維瘤病; 空腸平滑肌肉瘤; 消化道出血; Neurofibromatosis; Jejunal leiomyosarcorma; Gastrointestinal bleeding; |
語 文 | 中文(Chinese) |
中文摘要 | 神經纖維瘤病合併小腸平滑肌肉瘤是相當罕見的,在現有的文獻中,只有兩例曾 經被報告過。我們報告一例 23 歲的女性病人在診斷神經纖維瘤病 I 型 10 年後,因急性 消化道出血、發燒及腹痛來本院就診。電腦斷層掃描顯示在空腸有一中空囊狀內含氣液平面 的腫瘤,於是患者接受局部空腸切除術,病理的診斷為平滑肌肉瘤。手術追蹤至今兩年並無 局部復發或遠端轉移的情形,至於神經纖維瘤病合併小腸平滑肌肉瘤的發生起源目前仍無定 論。 |
英文摘要 | Leiomyosarcoma of the gastrointestinal tract is rare in von Recklinghausen's disease.Only two cases of intestinal leiomyosarcoma with von Recklinghausen's disease had been reported in the English literature.We here- in report the case of a 23-year-old woman with a 10 year history of von Recklinghausen's disease presented with hematochezia, fever and abdominal pain. The CT scan of abdomen showed a huge cystic neoplasm with air-fluid level in the intestine. The patient underwent segmental resection for a presumed jejunal neoplasm, and the histologic section revealed that it was a leiomyosarcoma. The patient had no local recurrence or distant metastasis after 2 years of follow-up. The histogenesis of leiomyosarcoma with neurofibromatosis is controversial. |
本系統中英文摘要資訊取自各篇刊載內容。