頁籤選單縮合
題 名 | 色素血管晶體樣瘤病IIb型合併右腎缺失畸形=Phakomatosis Pigmentovascularis Type IIb with Right Kidney Agenesis |
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作 者 | 黃靖媛; 李玉雲; 吳峻宇; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 16:2 1998.06[民87.06] |
頁 次 | 頁147-152 |
分類號 | 415.687 |
關鍵詞 | Phakomatosis pigmentovascularis; Port-wine stain; Mongolian spots; Melanosis oculi; |
語 文 | 中文(Chinese) |
中文摘要 | 本文報告一例罕見的色素血管晶體樣瘤病Ⅱb型合併右腎缺失。一位八歲的男孩因 泌尿道感染而住進本院,理學檢查發現廣泛的酒色斑,異常的蒙古斑,兩腳長度不同,骨盆 傾斜,脊柱側彎及雙眼球黑變症。完整的檢查顯示,右腎臟缺失畸形,在此病中尚未被報告 過。 |
英文摘要 | We report a rare case of phakomatosis pigmentovascularis(PPV), type Ⅱb, in association with right kidney agensis. An 8-year-old boy was admitted to our hospital for urinary tract infection. Extensive port-wine stain, aberrant Mongolian spots, leg-length discrepancy, pelvic obliquity, scoliosis and bilateral melanosis oculi bulbi were noted. Further investigation revealed right kidney agenesis which has never been observed in PPV. |
本系統中英文摘要資訊取自各篇刊載內容。