頁籤選單縮合
題 名 | 環毛囊纖維瘤=Perifollicular Fibroma |
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作 者 | 賴憲宏; 李婉若; 賴建仲; 林永和; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 16:3 1998.09[民87.09] |
頁 次 | 頁196-201 |
分類號 | 415.78 |
關鍵詞 | 環毛囊纖維瘤; Perifollicuar fibroma; Fibrofolliculoma; Trichodiscoma; |
語 文 | 中文(Chinese) |
中文摘要 | 本文報告一環毛囊纖維瘤的病例。病患為一 44 歲女性,近三年來於臉上及頸部 出現許多無症狀性、膚色、稍為凸起的丘疹;病理切片下可見發育完好的毛囊被以同心圓層 狀的膠原纖維所包圍,這些膠原纖維含有多量的酸性黏多醣質,且其中沒有彈性纖維;病患 的哥哥及弟弟也有類似的皮膚表現。環毛囊纖維瘤是一由毛囊結締組織鞘膜所增生而來的皮 膚缺陷瘤,目前認為可能是經由體染色體顯性遺傳。我們提出這一典型病例並回顧過去發表 的文獻,另外也提出了一些不同的看法。 |
英文摘要 | Perifollicular fibroma (PFF) is a rare cutaneous hamartoma, which results from proliferation of the pilar connective tissue sheath. It is considered to be inherited by autosomal dominant trait. We report a case of PFF on a 44 y/o female, who presented with the cutaneous findings of multiple asymptomatic, flesh-colored, dome-shaped papules on the face and neck for 3 years. The histopathology revaled well-developed hair follicles surrounded by concentric arrangement of young collagens. These collagens were rich in acid mucopolysacchride and devoid of elastic fibers. Her brothers had similar skin lesions since adulthood. The related literatures are reviewed and we also propose some different opinions from previous publications. |
本系統中英文摘要資訊取自各篇刊載內容。