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頁籤選單縮合
題 名 | Congenital-infantile Fibrosarcoma: A Case Report=先天性幼兒纖維瘤:病例報告 |
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作 者 | 鄭旭萌; 施焄鏻; 許清寅; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 24:3 1999.06[民88.06] |
頁 次 | 頁131-134 |
分類號 | 417.509 |
關鍵詞 | 纖維瘤; 幼兒; 新生兒; 電腦斷層攝影; 小兒; 核磁共振攝影; Fibrosarcoma; Infants; Newborn; Computed tomography; CT; Pediatric; Magnetic resonance; MR; |
語 文 | 英文(English) |
中文摘要 | 先天性幼兒纖維瘤是一罕見而且值得特別注意的腫瘤。它和一般的纖維瘤不一樣在於它的臨床表現:預後通常很好,5年存活率可以到達80%以上。及早知道這個疾病,就有可能避免整肢切除的手術。我們報告一個患有右大腿無痛腫塊之新生兒病例。影像之各項各檢發現一界限不清楚並有骨頭破壞的腫塊。我們並且探討各影像檢查在診斷及治療之角色,CT及MRI皆對此腫瘤的影響範圍做出良好的事前評估。 |
英文摘要 | Congenital-infantile fibrosarcoma is a rare tumor with which clinicians should be familiar. Its clinical course differs from conventional fibrosarcoma, the prognosis is usually good and the 5-year survival rate can be more then 80%. With early recognition of this disease entity, aggressive excision such as limb-amputation can be avoided. We report a case of a newborn baby boy with a painless swollen mass in his right thigh. The imaging study of plain film, CT and MRI showed an ill-defined mass with bony destruction. Chemotherapy using oncoving, actinomycin-D and endoxan was performed after the diagnosis, the patient is doing well up to now. |
本系統中英文摘要資訊取自各篇刊載內容。