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題名 | 肝內膽管乳頭狀瘤病:一病例報告與文獻回顧=Intrahepatic Biliary Papillomatosis:A Case Report and Review of Literature |
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作者 | 王柏川; 王鴻源; 施壽全; 鄭國祥; 張國明; Wang, Po-chuan; Wang, Horng-yuan; Jenq, Gwo-shyang; Shy, Show-chyuan; Jang, gwo-ming; |
期刊 | 中華民國急救加護醫學會雜誌 |
出版日期 | 19970900 |
卷期 | 8:3 1997.09[民86.09] |
頁次 | 頁127-132 |
分類號 | 415.456 |
語文 | chi |
關鍵詞 | 膽管乳頭狀瘤病; 黏液分泌性腫瘤; 肝內膽道腫瘤; Biliary papillomatosis; Mucinous secretion tumor; Intrahepatic biliary tumor; |
中文摘要 | 肝內膽管乳頭狀瘤病,是非常罕見而且很難去定義的疾病。自1894年,Chappet首先描述這樣的疾病以來,到目前為止,世界上文獻中約有六十個病例被提出。本文報告一73歲女性病人,以上腹痛,發燒畏寒,輕度黃疸及體重減輕為臨床表現; 經超音波,電腦斷層檢查,發現有左側肝內膽管擴張而懷疑其內有腫瘤生成。經皮穿肝膽道引流,有許外黏液被引流出。手術中膽管鏡見有乳頭狀腫瘤在左側肝管內。最後由手術之組織病理證實為肝內膽管乳頭狀瘤。文中強調黏液分泌為肝內膽管乳頭狀肉瘤病的特性,且為術前正確診斷的重要線索。此腫瘤有癌化的可能,故治療上以外科手術為佳。若病灶侷限在肝臟一葉或一節,則更應優先考慮全葉切除,因其有治療的可能性。 |
英文摘要 | Intrahepatic biliary papillomatosis is a very rare and poorly defined disorder. Since the first description by Chappet in 1894, only about 60 cases have been reported in the world literature. We report the case of a 73-year-old female who visited our hospital with epigastralgia, fever, chills, mild jaundice and body weight loss. Dilated left intrahepatic ducts and a nodular lesion in the left intrahepatic duct were noted by imaging study including sonography and CT scanning. Much mucoid fluid was drained using a percutaneous transhepatic biliary drain. Intraoperative choledochoscopy revealed a papillary tumor in the left intrahepatic duct. Intrahepatic biliary papillomatosis was proven by pathology examination. We emphasize that mucus secretion is a characteristic of intrahepatic biliary papillomatosis and an important clue to assist in making an accurate diagnosis prior to operation. Because of its tendency to malignant transformation, surgical resection should be given priority over palliative treatment. If the lesion is localized to one segment or lobe of liver, lobectomy should be considered with the hope of a cure. |
本系統之摘要資訊系依該期刊論文摘要之資訊為主。