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題 名 | Well-Differentiated Fetal Adenocarcinoma: A Case Report=分化良好的肺臟胎兒腺癌:病例報告 |
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作 者 | 吳金珠; 蘇誠道; 陳良光; 彭惠玲; 盧大年; 李進成; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 28:6 2003.12[民92.12] |
頁 次 | 頁387-391 |
分類號 | 416.224 |
關鍵詞 | 複相的肺母細胞瘤; 電腦斷層攝影; 肺母細胞瘤; 分化良好的肺臟胎兒腺癌; Biphasic pulmonary blastoma; Computed tomography; Pulmonary blastoma; Well differentiated fetal adenocarcinoma; |
語 文 | 英文(English) |
中文摘要 | 肺母細胞瘤是一種發生於年輕人極為罕見的惡性腫瘤。其組織學圖像類似胎兒期肺組織,主要是由腺管樣排列或瀰漫樣分佈的間葉樣的腫瘤細胞所構成 肺母細胞瘤有兩種類型,分別為複相及單相的、即所謂的分化良好的肺臟胎兒腺癌。在此我們敘述一位28歲女性病患的臨床和影像表現。電腦斷層攝影顯示一邊緣清楚的腫瘤在右肺中葉,伴髓著壞死區域。最後經手術切除及病理檢驗後証實為分化良好的肺臟胎兒腺癌。對於這種腫瘤,手術切除還是為主要治療方式,至於化療和電療所伴演的角色,仍待商確。雖然此病例極為罕見,臨床上沒有特殊的症狀,手術前診斷也比較困難。然而、若一年輕患者其影像特徵為一界定清處的腫塊時,分化良好的肺臟胎兒腺癌必須列入鑑別診斷。 |
英文摘要 | Pulmonary tumors of embryonic origin are rare, in which pulmonary blastomas (PB) are probably the most uncommon. The two types of PB, biphasic and monophasic, are also known as well-differenti-ated fetal adenocarcinoma (WDFA). We recently encountered one patient with PB in a young adult. The histopathologic findings was consistent with the monophasic type of pulmonary blastoma – WDFA. There are no specific clinical or radiological features of WDFA, although young age, peripheral location of well circumscribed mass and large tumor size are often characterisitic findings. The histopathological and immunohistochemical techniques play an important role and are the only reliable way to establish a definite diagnosis. The surgical resection is the treatment of choice. |
本系統中英文摘要資訊取自各篇刊載內容。