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題 名 | Propofol Anesthesia in a Patient with Isaacs Syndrome--Report of a Case and Literature Review=Isaacs症候群麻醉:病例報告與文獻回顧 |
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作 者 | 石明煌; 何綺月; 林志中; 徐魁堯; 楊承憲; 陳介絢; | 書刊名 | 麻醉學雜誌 |
卷 期 | 35:4 1997.12[民86.12] |
頁 次 | 頁241-245 |
分類號 | 416.5 |
關鍵詞 | 麻醉劑; 靜脈注射:Propofol; 運動神經元疾病:Isaacs症候群; Anesthetics; Intravenous:Propofol; Motor neuron disease:Isaacs syndrome; |
語 文 | 英文(English) |
中文摘要 | Isaacs症候群是一種少見的下運動神經元疾病,其產生原因不明。臨床上,Isaacs 症候群特性包括肌肉痙攣、僵直、與肌腱反射性減弱。由於臨床上極少見到,文獻上對麻醉 之描述極少,因此本病例報告對丈獻做一些探討,並提出與麻醉相關之討論。本病例是一患 有Isaacs症候群之病患,因患有扁桃腺炎,由於扁桃腺過大有阻塞呼吸道之虞,需進行雙側 扁桃腺切除術,由於此病患之前的藥物控制不理想,在麻醉前仍有不自主的肌內痙攣。本病 例針對此病患之麻醉經過與麻醉考量,並與文獻比較討論此罕見病例之麻醉注意事項。 |
英文摘要 | Isaacs syndrome is an unusual lower motor neuron disease characterized by myokymia (muscle twitching), muscular stiffness, and decreased tendon reflexes, We reported a patient who was affected with this rare disease, with manifestation of involuntary muscular contractions and required general anesthesia for bilateral tonsillectomies. Understanding the presentation and characterization of this unusual disease may be helpful in making choice of anesthetics or anesthetic techniques. Its possible mechanisms of action and its specific considerations in anes- thesia in the literature are reviewed and discussed. |
本系統中英文摘要資訊取自各篇刊載內容。