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題 名 | Primary Malignant Fibrous Histiocytoma in Uremic Kidney: A Case Report and Literature Review=原發性惡性纖維組織細胞瘤發生在尿毒腎臟之病例報告及文獻回顧 |
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作 者 | 查岱龍; 孫光煥; 張保欽; 馬正平; 張聖原; 于大雄; | 書刊名 | 中華民國外科醫學會雜誌 |
卷 期 | 31:3 民87.05-06 |
頁 次 | 頁200-205 |
分類號 | 416.273 |
關鍵詞 | 惡性纖維組織細胞瘤; 腎臟; Renal neoplasm; Malignant fibrous histiocytoma; Sarcoma; |
語 文 | 英文(English) |
中文摘要 | 一位五十八歲接受洗腎之男性尿毒症患者,最近一個月因間歇性血尿及右側腰痛 而就診;影像學檢查發現為一右側腎臟腫瘤合併腎靜脈腫瘤血栓,患者接受根除性腎臟切除 術,且組織病理學顯示為惡性纖維組織細胞瘤。惡性纖維組織細胞瘤是軟組織肉瘤中最常見 者,其好發於肢體近端但卻極少發生於腎臟,特別是尿毒症的患者。在以往的英文文獻中, 僅二十位原發性腎臟惡性纖維組織細胞瘤患者曾被報告,但沒有一位是尿毒症患者;因此我們 報告此一病例,以探討此一罕見疾病之臨床表徵、診斷及其治療。 |
英文摘要 | A 58-year-old uremic man with regular hemodialysis presented with intermittent gross hematuria and right flank pain lasting for one month. Imaging studies revealed a right renal mass with tumor thrombi in the renal vein. Radical nephrectomy was performed and the histopathology revealed a malignant fibrous histiocytoma. Although malignant fibrous histiocytoma (MFH) is the most common type of malignancy originating from soft tissues, often occuring in the proximal side of the limbs, it rarely originates in the kidney, particularly in a uremic patient. Only twenty cases of primary renal MFH have been reported in the previous English literature, but none were uremic. Herein, we report this case and discuss the clinical picture, diagnosis and treatment aspects of this rare disease entity. |
本系統中英文摘要資訊取自各篇刊載內容。