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題 名 | Oral Manifestations of Burkitt's Lymphoma--Cases Report=柏奇特氏淋巴瘤之口腔表徵--病例報告 |
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作 者 | 郭舜卿; 盧心玉; | 書刊名 | 中華牙醫學雜誌 |
卷 期 | 18:3 1999.09[民88.09] |
頁 次 | 頁217-228 |
分類號 | 416.94 |
關鍵詞 | 柏奇特氏淋巴瘤; Burkitt's lymphoma; |
語 文 | 英文(English) |
中文摘要 | 柏奇特氏淋巴瘤是一罕見且極度惡性的腫瘤,雖然主要侵犯赤道非洲兒童,但是 許多國家都有病例發生,包括臺灣幾個罕見的個案報告。柏奇特氏淋巴瘤是人類腫瘤中生長 最迅速者,以多發性廣泛侵犯淋巴結以外的組織器官為其生長特性,病情發展極快,如果不 予以及時治療會迅速致命。成功的治療全靠早期診斷及有效控制的化學療法。本文報告具有 典型臨床症狀及病理特徵的柏奇特氏淋巴瘤病例。分別是二歲男童,七歲女童與十一歲男童 ,三例口腔特徵均表現:(1)不同程度的顎骨侵犯,(2)齒齦及齒槽骨腫大,(3)牙齒 鬆動移位,(4)�琱�提前萌出。全身性 症狀有:(1)發燒、倦怠,(2)食慾不振、體重 減輕,( 3 )腹部腫瘤,( 4 )肝脾與淋巴結腫大。二例有骨髓侵犯者,因拒絕治療,出 院一個月內死亡。一例接受化學治療效果良好,卻因痲疹併發肺炎,心肺衰竭而死亡。本文 特別回顧文獻並就牙醫師對顎骨侵犯時口腔重要表徵於早期診斷上所扮演角色加以討論。 |
英文摘要 | Burkitt's lymphoma is a rare and extremely malignant tumor that often affects children. Clinically, the tumor is characterized by very rapid growth and progression of symptoms with multifocal extranodal involvement in areas such as the jaw, abdominal viscera, bone marrow, and central nervous system. It is the fastest growing human tumor with a rapid and lethal clinical course. The successful treatment of Burkitt's lymphoma depends on a combination of early diagnosis and effective controlled chemot erapy. When jaw involvement occurs, the majority of patients are seen initially by dentists for treatment of oral and dental symptoms. Therefore, dentists play a very important role in the early diagnosis of Burkitt's lymphoma with jaw lesions by recognizing the clinical oral manifestations coupled with characteristic radiographic signs. We report three cases of Burkitt's lymphoma with typical clinical, radiographic and histological features. The patients were a 2-year-old boy, a 7-year-old girl, and an 11- year-old boy. At presentation, the extent of their abdomen and jaw involvement varied. Two boys also presented with bone marrow involvement and died within one month after discharge because their families refused chemotherapy. The 7-year-old girl showed early dramatic response to chemotherapy but eventually died six weeks after initial diagnosis because of measles infection resulting in pneumonia and respiratory failure. It is important that patients with Bukitt's lymphoma be correctly diagnosed early and r eceive effective chemotherapy because prognosis and prolonged survival are associated with the extent of tumor at initiation of treatment. Misdiagnosis and delayed treatment are common with Burkitt's lymphoma. Dentists should be familiar with Burkitt's lymphoma and its clinical oral manifestations. |
本系統中英文摘要資訊取自各篇刊載內容。