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題 名 | Intracortical Osteosarcoma: Report of a Case=骨皮質中骨肉瘤:一病例報告 |
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作 者 | 楊曙華; 吳振都; 王全正; 郭明勳; 楊榮森; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 99:9 2000.09[民89.09] |
頁 次 | 頁721-725 |
分類號 | 416.66 |
關鍵詞 | 骨皮質; 骨肉瘤; Intracortical osteosarcoma; En bloc resection; Chemotherapy; Malignant bone sarcoma; |
語 文 | 英文(English) |
英文摘要 | Abstract: Intracortical osteosarcoma is the rarest anatomic variation of osteosarcoma. There have been only 12 cases reported in the English-language literature. We present a case of osteosarcoma in an 18-year-old Taiwanese man that originated within the cortex of the tibial diaphysis. The in tial radiograph revealed a lytic mass confined to the cortex, mimicking a benign bone lesion. Histopathologic examination of the biopsy specimen showed and osteoblasic osteosarcoma mingled with some fibroblastic foci. He underwent en bloc resection, and a metallic prosthetic intercalary stem was used to replace the larger bone defect. Adjuvant chemotherapy was administered before and after the operation. He was free of disease during 40 months of follow-up. A review of all reported cases of intracortical osteosarcoma revealed that the initial method of treatment plays an important role in local recurrence and distant metastasis. Local excision and curettage leads to the worst results. The outcomes of more recently reported cases have improved because of early awareness of the possibility of malignancy and advances in chemotherapy. However, whether patients with intracortical osteosarcoma have a different prognosis from those with conventional osteosarcoma cannot be determined, because of the small number of intracortical osteosarcoma cases available for analysis. |
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