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題 名 | Systemic Penicillium Marneffei Infection in a Child with Common Variable Immunodeficiency=尋常變異性免疫缺陷孩童罹患全身性青黴菌感染 |
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作 者 | 林文川; 戴仰霞; 蔡銘哲; 黃立民; 江伯倫; | 書刊名 | 臺灣醫學會雜誌 |
卷 期 | 97:11 1998.11[民87.11] |
頁 次 | 頁780-783 |
分類號 | 415.944 |
關鍵詞 | 尋常變異性免疫缺陷孩童; 全身性青黴菌感染; Common variable immunodeficiency; Penicillium marneffei; Juvenile rheumatoid arthritis; |
語 文 | 英文(English) |
英文摘要 | Penicillium marneffei is rarely pathogenic in humans. Most previously reported cases of P. marneffei infection were from Southeast Asia where patients were usually in an immunocompromised state due to human immunodeficiency virus (HIV) infection. The majority of the patients reported in Western countries were immunocompromised by malignancy, especially Hodgkin's lymphoma. In Taiwan, the first case of P. marneffei infection was reported in 1994 and involved an adult with HIV infection. We report a case of systemic P. marneffei infection in a child with common variable immunodeficiency (CVID). The patient, a 4-year, 5-monthold boy, had a 1-year history of oligoarthritis resembling juvenile rheumatoid arthritis (JRA). He developed a low grade fever (38℃) and hepatosplenomegaly 1 month before admission to the hospital. Although cultures of synovial fluid obtained at the time of onset of oligoarthritis did not grow any organisms, cultures of blood, bone marrow, synovial fluid, and lymph node biopsy samples taken during this admission were positive for P. marneffei. Futher immunologic studies revealed a profile characteristic of CVID. The fungal infection was finally eradicated by combined therapy with amphotericin B, fluconazole, itraconazole, itraconazole, and regular immunoglobulin replacement. This case reminds us that JRA or JRA-like arthritis should be differentiated from septic arthritis caused by rare pathogens in immunocompromised patients. |
本系統中英文摘要資訊取自各篇刊載內容。