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題 名 | Primary Synovial Sarcoma of the Kidney: A Case Report=腎臟原發性滑液肉瘤:病例報告 |
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作 者 | 崔祐堃; 林重榮; 王家槐; 沈書慧; 潘競成; 張延驊; 張政彥; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 29:6 2004.12[民93.12] |
頁 次 | 頁359-363 |
分類號 | 415.818 |
關鍵詞 | 腎腫瘤磁振造影; 腎臟滑液肉瘤; Kidney neoplasms MR; Synovial sarcoma; |
語 文 | 英文(English) |
中文摘要 | 腎臟原發性滑液肉瘤是一種罕見的腎臟腫瘤。t(18,x)的染色體轉位是這個疾病的特徵。我們在此報告一個腎臟原發性滑液肉瘤伴隨有以下轉移的影像特徵:腫瘤佔據整個左腎,侵入左邊腎靜脈以及下腔靜脈,並且腫瘤栓塞向上延伸到右心房與向下到腎臟下段下腔靜脈。後腹腔膨大的淋巴結也被發現。在肝臟發現有結節病灶,考慮肝轉移的可能。病理診斷經由RT-PCR顯示出與t(X;18)染色體轉位有關的SYT-SSX基因轉錄,確定為腎臟原發性滑液肉瘤。腎臟原發性滑液肉瘤只能經由分子分析來確認。對於我們而言,很難單由影像檢查去與其他原發性腎臟腫瘤做鑑別診斷。當在年輕成年人發現腎臟腫瘤具有侵襲性的表現,如局部膨大淋巴結,腎靜脈侵犯,與遠端轉移時,提醒我們考慮這種不常見腎臟肉瘤的可能性。 |
英文摘要 | Primary synovial sarcoma of the kidney is a rare renal malignancy. A chromosomal translocation, t(X;18), is characteristic of this disease. We report a case of primary synovial sarcoma of the kidney showing the following imaging patterns: The tumor occupied the entire left kidney, invaded into the left renal vein and inferior vena cava, and the tumor thrombus extends upward to the level of right atrium, downward to infrarenal IVC. Enlarged lymph nodes were noted in the retroperitoneum. Nodular lesions were also noted in the liver and the possibility of liver metastasis was considered. The SYT-SSX fusion transcripts associated with the t(X;18) translocation was demonstrated by RT-PCR and the diagnosis of primary synovial sarcoma was confirmed by pathology. Primary synovial sarcoma of the kidney can only be confirmed by molecular analysis. It is difficult for the radiologist to differentiate renal synovial sarcoma from other primary renal tumors by image studies. The presence of renal tumor with invasive behavior, including regional lymphadenopathy, renal vein invasion, and distant metastasis, in young adult, should alert radiologist the possibility of this unusual renal sarcoma. |
本系統中英文摘要資訊取自各篇刊載內容。