頁籤選單縮合
題 名 | Extramedullary Plasmacytoma of the Head and Neck=頭頸部骨髓外漿細胞瘤 |
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作 者 | 邱文龍; 陳麗惠; | 書刊名 | 長庚醫學 |
卷 期 | 17:4 1994.12[民83.12] |
頁 次 | 頁378-383 |
分類號 | 416.21 |
關鍵詞 | Plasma cell neoplasm; Extramedullary plasmacytoma; M-protein; |
語 文 | 英文(English) |
中文摘要 | 骨髓外漿細胞瘤是一種罕見的細胞腫瘤,好發於頭頸部軟組織。本報告係回溯長庚醫院自民國六十七年至八十一年,十五年期間,總計有七例經病理和臨床分析證實為頭頸部骨髓外漿細胞瘤。七例均為男性,年齡由27至66歲,其中五例至清中有副蛋白質(M-protein) (三例為IgG-kappa型,一例為IgG-lambda型,另一例為lambda輕鏈型)。六例接受局部放射治療,三例接受化學治療,七例至今均存活(存活期間自37個月至116個月不等)。一例於九年後在頸部淋巴節復發,另一例(未接受射治療)發展為多發性骨髓瘤,其餘五例至今無復發跡象。根據我們的病例分析和文獻的回顧,我們認為以放射治療原發病灶及其局部淋巴節是治療本病的最好方法。如果腫瘤有進行性惡化,復發或擴散,則考慮使用化學治療。至於腫瘤是否得到良好控制或一直惡化,血清中之七蛋白質值是一有用評估標記。 |
英文摘要 | Extrameduallary plasmacytoma (EMP) is an uncommon malignant plasma cell neoplasm which usually presents as soft tissue mass in the head and neck. We retrospectively reviewed 7 cases with EMP of the head and neck between 1978 and 1992. All patients were male. Their ages ranged from 27 to 66 years. M-protein was identified in 5 patients (IgG-kappa in 3, IgG-lambda in 1 and Lambda light chain in 1). All but one were treated with local irradiation. Three patients revived chemotherapy. All patients have been alive for 37+ to 116+ months since the diagnosis of EMP. One patient had a cervical node recurrence 9 years after local irradiation and the other one who refused local irradiation but received chemotherapy developed multiple myeloma 5 years later. Based on our experience and the review of the literature, it is recommened that irradiation to the primary sites and the involved crevicall nodes is the treatment of choice. Additional chemotherapy may be considered in patients with disease progression, recurrence, or dissemination. The m-protein is a useful parameter to assess tumor control or disease progression. |
本系統中英文摘要資訊取自各篇刊載內容。