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頁籤選單縮合
題 名 | Congenital Esophageal Stenosis with Long Term Follow up: Report of a Case=先天性食道狹窄長期追蹤:病例報告 |
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作 者 | 陳政隆; 江榮華; 周定遠; | 書刊名 | 臺灣外科醫學會雜誌 |
卷 期 | 40:6 2007.11-12[民96.11-12] |
頁 次 | 頁265-270 |
分類號 | 416.241 |
關鍵詞 | 食道狹窄; Congenital esophageal stenosis; Fibromuscular stenosis; |
語 文 | 英文(English) |
中文摘要 | 一位足月出生女嬰只能慢慢餵食半奶,快速餵食會引起反嘔及噎食。當六個月大開始餵食固體食物時,立刻反嘔,吐出已吞的食物,因此只能吞食流質食物。四歲時,食道攝影顯示食道中段部分狹窄。病人在六歲,體重只有十五公斤,才接受外科治療。首先試圖使用通條擴張食道失敗後,以手術切除狹窄段,再端端吻合兩斷端。病人手術後可吞食固體物。病理檢查切除之食道顯示:長1.6公分、外徑1.2公分、內徑0.2公分、黏膜正常、黏膜下肌肉層增生、肥大、排列紊亂、軟組織廣泛性纖維化,診斷爲先天性纖維肌肉狹窄。術後病人發育成長正常。青春期以後,吞食大塊肉類時稍有遲滯感覺。食道鏡檢查及食道攝影顯示吻合處疤痕形成輕度狹窄。她未接受進一步的處置,只是避免吞嚥大塊肉類。 |
英文摘要 | Congenital esophageal stenosis is a rare entity, its incidence is much lower than that of congenital esophageal atresia. We report a full term normally delivered female infant who could only be fed with milk slowly after birth. Rapid feeding caused choking and regurgitation. She could tolerate liquid diet only. Esophagography at 4 years of age showed a short segmental stenosis at middle esophagus. The patient underwent surgical intervention at age 6 when her body weight was only 15 kilograms. Segmental resection of stenosis with primary end-to-end anastomosis was done after failure to dilate with a bougie. Pathological examination of the resected specimen showed congenital fibromuscular stenosis. After the operation the patient could eat solid foods and gained weight normally. As a teenager, she began to experience mild stasis in swallowing large pieces of meat. Both esophagoscopy and esophagography 18 years after operation showed a mild ringed narrowing at the anastomotic site. She received no further management but avoided swallowing large pieces of meat. |
本系統中英文摘要資訊取自各篇刊載內容。