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題 名 | Steroid-Dependent Sensorineural Hearing Loss without an Autoimmune Disease: Case Report and Review of the Literature=無自體免疫疾病之類固醇依賴型感音性聽力損傷:病例報告與文獻回顧 |
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作 者 | 張淯淞; 林明毅; 張國平; | 書刊名 | 臺灣耳鼻喉頭頸外科雜誌 |
卷 期 | 52:3 2017.07-09[民106.07-09] |
頁 次 | 頁114-117 |
分類號 | 416.897 |
關鍵詞 | 類固醇依賴型感音性聽力損傷; 病因不明突發性感音性聽力損傷; 自體免疫疾病; Steroid-dependent sensorineural hearing loss; Idiopathic sudden sensorineural hearing loss; Autoimmune disorder; |
語 文 | 英文(English) |
中文摘要 | 51歲男性因右側急性聽力損傷入院。初步臆斷為病因不明突發性感音性聽力損傷,因此先給予高劑量類固醇治療。治療後純音聽力檢查顯示反應良好,然而聽力隨著藥物減量惡化,並隨著給予的類固醇劑量波動。抽血檢查自體免疫抗體均為陰性,腦部核磁共振影像檢查正常。患者因出現顯著類固醇治療副作用,經討論改以鼓室內類固醇注射治療但療效不佳。因此,建議改以長期系統性類固醇治療。類固醇依賴型感音性聽力損傷為罕見造成急性感音性聽力損傷的疾病,通常需要數年的類固醇治療。此疾病可依系統性自體免疫疾病的有無分成二類,聽力預後依分型而有差異。此類患者需要長期追蹤,因可能會有緩慢漸進的聽力惡化。 |
英文摘要 | A 51-year-old man was admitted to this hospital because of right sudden hearing loss without associated symptoms. Idiopathic sudden sensorineural hearing loss (ISSNHL) was suspected and high-dose systemic steroid was administered. The symptoms improved initially. However, the hearing level deteriorated after tapering the steroid and fluctuated with the adjustment of dosage. Surveys including autoimmune markers and magnetic resonance imaging (MRI) were normal. Due to significant side effects of steroid, alternative therapy with intratympanic steroid injection (ITSI) was attempted but showed no benefit. Hence, long-term oral steroid was recommended. Steroid-dependent sensorineural hearing loss (SDSNHL) is a rare disorder that requires systemic steroid treatment for years. It could be classified for two types according to the presence of concomitant autoimmune disorders or not and the classification is related to the prognosis of hearing. Patient should be followed for a long period because gradual deterioration of hearing is possible. |
本系統中英文摘要資訊取自各篇刊載內容。