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題 名 | Alveolar Soft Part Sarcoma: Clinical Experience in VGHTPE=肺泡樣軟組織肉瘤--臺北榮民總醫院臨床治療經驗 |
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作 者 | 廖文傑; 林進德; 馬旭; 林素娥; | 書刊名 | 臺灣整形外科醫學會雜誌 |
卷 期 | 19:3 2010.09[民99.09] |
頁 次 | 頁189-198 |
分類號 | 415.148 |
關鍵詞 | 肺泡樣軟組織肉瘤; Alveolar soft part sarcoma; |
語 文 | 英文(English) |
中文摘要 | 背景:肺泡樣軟組織肉瘤是臨床上罕見的腫瘤,佔所有成人軟組織肉瘤0.5-0.9%,孩童軟組織肉瘤0.8-1.85%。臨床上治療經驗文獻記載並不多見。目的:我們提出臨床上治療肺泡樣軟組織肉瘤經驗並加以分析討論。材料及方法:從1975到2008,共有23位肺泡樣軟組織肉瘤病患在台北榮民總醫院接受治療,我們利用回溯分析其肉瘤特性及其臨床上治療。結果: 23位肺泡樣軟組織肉瘤病患平均年齡24歲(13-66 years)。肉瘤發生位置包括下肢13例、上肢4例、頭頸部2例、腹部1例、胸壁1例、背部1例、腰部1例。病例平均追蹤110(2-301)個月。平均存活48個月,五年存活率爲62%。5位肺泡樣軟組織肉瘤病患初次確定診斷時已經出現腫瘤轉移,15位肺泡樣軟組織肉瘤病患出現肺部轉移,9位初次確定診斷時已經出現腫瘤轉移。出現腫瘤轉移病患平均存活38.5個月。結論:肺泡樣軟組織肉瘤好發在年輕病患年齡,確定診斷時已經出現腫瘤轉移預後較差,但是經由適當治療長期存活是可能的。 |
英文摘要 | Background: Alveolar soft part sarcoma (ASPS) is rare malignant tumor constituting 0.5-0.9% of all soft tissue sarcomas in adults and 0.8-1.85 of those in children. Published series on presentation and treatment outcome of this sarcoma are scarce. Aim and Objectives: We present our experience in treating patients with this disease. The clinical features, diagnosis, treatment and prognostic factors of patients with ASPS were studied. Materials and Methods: Between 1975 and 2008, 23 patients with alveolar soft part sarcoma were treated in our hospital. We collected the files and described their characteristics, therapy and course. Reslts: The study group consisted of 11 male and 12 female patients, the median age at diagnosis was 24 years (13-66 years). The primary site was the lower extremity (n=13), upper extremity (n=4), head and neck (n=2), abdominal wall (n=1), chest wall (n=1), back (n=1) and flank (n=1). The median follow-up was 110(2-301) months. The median survival was 48 months with an overall 5-year survival of 62%. At time of diagnosis 5 patients already had metastases. Fifteen patients (65%) suffered from lung metastasis. Among them 9 of 15 patients had lung metastasis at the initial diagnosis, 6 patients developed lung metastasis later. Median survival after diagnosis of metastases was 38.5 (1-101) months. Conclusion: Alveolar soft part sarcoma is found especially in young adults. When diagnosed it is often metastasized with a poor prognosis. However, with adequate treatment, long-term survival is possible. |
本系統中英文摘要資訊取自各篇刊載內容。