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題 名 | Hodgkin's Lymphoma Presenting as Idiopathic Cholestatic Jaundice=以膽汁淤積為表現之何杰金氏淋巴癌 |
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作 者 | 洪崇霖; 蔡瑞鴻; 王韋淯; 李艷林; 吳尚殷; 葉裕民; 邱威鑫; 林鵬展; 蘇文彬; 顏家瑞; 陳雅萍; 蘇五洲; 陳彩雲; | 書刊名 | 臺灣癌症醫學雜誌 |
卷 期 | 26:4 2010.08[民99.08] |
頁 次 | 頁174-178 |
分類號 | 415.6 |
關鍵詞 | 膽汁淤積; 何杰金氏淋巴癌; 黃疸; Cholestasis; Hodgkin's lymphoma; Jaundice; |
語 文 | 英文(English) |
中文摘要 | 原發性膽汁淤積是何杰金氏淋巴癌少見的表現。我們報告一位26 歲的男性,被診斷 為第三期何杰金氏淋巴癌合併黃疸。經過診斷檢查之後,排除了其他可能會造成黃膽的 原因,因此診斷為何杰金氏淋巴癌合併有原發性膽汁淤積的表現。由於膽色素高達 30mg/dL,病人先接受放射線治療。膽色素在放射治療之後逐漸下降,因此我們接著給予 標準的化學治療。經過完整的化學治療之後,淋巴癌達到部份緩解,而病人的膽色素也 下降至正常,目前持續在門診追蹤。總結來說,原發性膽汁淤積唯一排除性的診斷,而 針對淋巴癌的緩解引導對於保存肝功能以及長期存活有相當大的影響。 |
英文摘要 | Background: Idiopathic cholestasis is a rare presentation of Hodgkin’s lymphoma. We report a case with this diagnosis and review the literature. Case Description: A 26-year-old male presented with Hodgkin’s lymphoma, stage IIIs with elevated serum bilirubin level up to 30 mg/dL. Idiopathic cholestasis was diagnosed after exclusion of other possibilities of jaundice. Radiotherapy was performed first, and the cholestasis gradually improved, which allowed subsequent standard systemic chemotherapy. After completion of chemotherapy, the disease status was partial remission, and the patient’s serum bilirubin level returned to normal. He was alive and free of recurrence 16 months after diagnosis. Conclusions: Idiopathic cholestasis is a diagnosis of exclusion. Prompt remission induction provides the chance to liver function recovery and long-term survival. |
本系統中英文摘要資訊取自各篇刊載內容。