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頁籤選單縮合
題名 | 嗜伊紅性白血球增多症 |
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作者姓名(中文) | 胡名宏; 高志平; | 書刊名 | 臨床醫學 |
卷期 | 68:3=405 2011.09[民100.09] |
頁次 | 頁211-222 |
分類號 | 415.635 |
關鍵詞 | 嗜伊紅性白血球增多症; 嗜伊紅性白血球增多症候群; 骨髓增生性腫瘤; Eosinophilia; Hypereosinophilia syndrome; HES; Myeloproliferative neoplasms; MPNs; |
語文 | 中文(Chinese) |
中文摘要 | 嗜伊紅性白血球增多症(acquired eosinophilia)分成次發性(secondary)、單株性(clonal)和原發性(idiopathic)三大類。次發性嗜伊紅性白血球增多症造成的原因包括寄生蟲感染、過敏、血管炎、藥物和淋巴腫瘤等等。單株性有特定骨髓性惡性腫瘤(myeloid malignancy)組織型態(histologic)、細胞(cytogenic)和分子(molecular)的表現。世界衛生組織(World Heath Organization,WHO)血液腫瘤的分類中,主要有兩種血液腫瘤的表現是以單株性嗜伊紅性白血球為主,分別是慢性嗜伊紅性白血球白血病(chronic eosinophilic leukemia, not otherwise specified, CEL-NOS)和PDGFRA PDGFRB 或是FGFR1陽性的骨髓性腫瘤(myeloid neoplasms associated with eosinophilia and abnormalities of PDGFRA (alpha type platelet-derived growth factor receptor), PDGFRB (beta type platelet-derived growth factor receptor) or FGFR1 (fibroblast growth factor receptor 1))。嗜伊紅性白血球增多症候群(hypereosinophilic syndrome, HES)屬於原發性嗜伊紅性白血球增多症的其中一種,和單純的嗜伊紅性白血球增多(hypereosinophilia)不同的是HES合併有嗜伊紅性白血球造成的器官傷害(eosinophilia-related organ damage)。 |
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