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題 名 | Juvenile Idiopathic Arthritis Presenting with Prolonged Fever |
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作 者 | Yeh, Tzu-lin; Huang, Fu-yuan; Shyur, Shyh-dar; Chen, Tien-ling; Lee, Chyou-shen; Huang, Daniel Tsung-ning; | 書刊名 | Journal of Microbiology, Immunology and Infection |
卷 期 | 43:3 2010.06[民99.06] |
頁 次 | 頁169-174 |
分類號 | 416.61 |
關鍵詞 | Clinical manifestation; Fever; Systemic-onset juvenile idiopathic arthritis; |
語 文 | 英文(English) |
英文摘要 | Systemic-onset juvenile idiopathic arthritis (s-JIA) is a systemic disease often accompanied by a fever. We examined 16 patients with s-JIA and reported the clinical manifestations, laboratory data, treatments and outcomes. METHODS: From 1984 to 2007, 16 children (aged 1–16 years), who were diagnosed as having s-JIA, were admitted to the Mackay Memorial Hospital in Taiwan. We retrospectively reviewed their medical charts. RESULTS: There were nine boys and seven girls, with mean age of onset of 7.4 ± 5.5 years. Fever (100%), typical rash (63%), and arthritis (75%) were the three most common symptoms. Lymphadenopathy (50%), hepatosplenomegaly (63%), pleural pulmonary manifestations (13%) and myalgia (25%) were also noted. One patient had Epstein-Barr virus-associated hemophagocytic syndrome complications. Neutrophilic leukocytosis was a common feature. Other laboratory data showed elevated C-reactive protein levels (25.1 ± 50.3 mg/dL), and erythrocyte sedimentation rates (69 ± 28 mm/hr) and abnormal liver enzymes. Marked hyperferritinemia (> 2,000 ng/mL) was noted in 57% (4/7) of the patients. The mean time from onset of symptoms to diagnosis was 9.2 weeks. Non-steroidal anti-inflammatory drugs, steroids, diseasemodifying anti-rheumatic drugs and anti-tumor necrosis factor agents were used for treatment. Due to prolonged fever, 2.0 ± 1.6 (maximum = 5) different kinds of antibiotics were used before a diagnosis was made. Most cases had satisfactory therapeutic outcomes except one boy, who had permanent joint contracture. CONCLUSION: The clinical manifestations of s-JIA in Taiwan were often accompanied by a prolonged fever. This results in clinicians often suspecting bacterial infections and prescribing several kinds of antibiotics. In the case of prolonged fever, s-JIA should always be placed on the list of differential diagnoses. |
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