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頁籤選單縮合
題 名 | Extreme Hypernatremia Combined With Rhabdomyolysis and Acute Renal Failure=極高血鈉併發橫紋肌溶解症與急性腎衰竭 |
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作 者 | 楊姿瀅; 張瑞文; 曾敏華; 王馨慧; 牛道民; 楊令瑀; | 書刊名 | Journal of the Chinese Medical Association |
卷 期 | 72:10 2009.10[民98.10] |
頁 次 | 頁555-558+CA105 |
分類號 | 415.815 |
關鍵詞 | 急性腎衰竭; 先天中樞性換氣不足症候群; 高血鈉; 腦下垂體低下症候群; 橫紋肌溶解症; Acute renal failure; Congenital central hypoventilation syndrome; Hypernatremia; Hypothalamus dysfunction syndrome; Rhabdomyolysis; |
語 文 | 英文(English) |
英文摘要 | Rhabdomyolysis is a life-threatening condition that involves muscle cell destruction. Among its etiologies, severe hypernatremia is a less common cause. We report a teenage girl with congenital central hypoventilation syndrome and hypothalamus dysfunction syndrome who presented with extreme hypernatremia (sodium, 211 mmol/L) with rhabdomyolysis (creatine kinase, 32,850 U/L) and acute renal failure (creatinine, 6.1 mg/dL) following gastroenteritis with 7-kg weight loss. Rhabdomyolysis subsequently led to acute renal failure and hyperkalemia. Acute hemodialysis was initiated on hospital day 3 for hyperkalemia. This resulted in a 13 mmol/L fall in serum sodium in 3 hours despite using a 156 mmol/L sodium bath, but without the development of cerebral edema or neurological defect. This report highlights an unusual cause of rhabdomyolysis in children and the experience of managing such a difficult clinical situation. |
本系統中英文摘要資訊取自各篇刊載內容。