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題 名 | Sonographic Features of Eosinophilic Fasciitis with Asymmetrical Symptoms: A Case Report=非對稱性嗜伊紅性筋膜炎的超音波表現:病例報告 |
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作 者 | 陳彥豪; 梁蕙雯; 王亭貴; | 書刊名 | 臺灣復健醫學雜誌 |
卷 期 | 40:2 2012.06[民101.06] |
頁 次 | 頁91-95 |
分類號 | 415.699 |
關鍵詞 | 嗜伊紅性筋膜炎; 超音波; 風濕免疫疾病; Eosinophilic fasciitis; Sonography; Rheumatological disorder; |
語 文 | 英文(English) |
中文摘要 | 嗜伊紅性筋膜炎(eosinophilic fasciitis)是一種相當少見的風濕免疫疾病,臨床表現有肌肉疼痛、對稱性手腳局部皮膚硬化、以及周圍血液嗜伊紅性白血球數量上升。因為此疾病與其他免疫風濕性疾病之症狀多所重複,因此,早期診斷不易,確診需倚賴全皮層皮膚切片檢查。影像學檢查也用於協助評估診斷,而超音波對於軟組織具高解像力、且取得方便,讓它在診斷嗜伊紅性筋膜炎的可用性不輸於核磁共振造影,然而,過去極少文獻提出嗜伊紅性筋膜炎的超音波影像表現。本文報告一位24歲女性,出現少見的非對稱性症狀,包括左手腕/手部攣縮以及右小腿與軀幹的緊繃,在初始症狀發生後一年半,經全皮層皮膚切片病理診斷為嗜伊紅性筋膜炎。超音波檢查顯示左手掌腱鞘明顯增厚、回音減少,右側腓腸肌的表淺筋膜增厚。經過類固醇治療八個月,左側手腕/手部攣縮改善,超音波的表現也趨於正常。 |
英文摘要 | Eosinophilic fasciitis is a rare rheumatological disorder, with the clinical presentations of myalgia, symmetrical skin induration, and peripheral eosinophilia. Because of overlapping symptoms with other rheumatological disorders, early diagnosis of eosinophilic fasciitis is difficult. The confirmatory diagnosis relies on full-thickness skin biopsy. Imaging studies are also used for evaluation and diagnosis. Among them, high-resolution sonography has the advantage of high accessibility over other imaging modalities in detecting musculoskeletal disorder, but the sonographic features of eosinophilic fasciitis are rarely reported. This study reported a 24-year-old woman who was diagnosed as eosinophilic fasciitis with rare presentation of asymmetric involvement. She had left wrist/hand contracture and a tightness sensation at the right calf and trunk. Diagnosis was confirmed by a full-thickness skin biopsy 1.5 years after initial symptoms. The ultrasound showed marked thickening of the tendon sheaths of the flexor tendons with reduced echogenecity at the level of metacarpal bones in a transverse view. Thickening of the superficial fascia was also present at the right gastrocnemius. After treatment with prednisolone for 8 months, the wrist and hand contracture improved and the sonographic findings normalized. |
本系統中英文摘要資訊取自各篇刊載內容。