查詢結果分析
相關文獻
頁籤選單縮合
題 名 | Adult-onset Still's Disease Complicated with Hemophagocytic Syndrome |
---|---|
作 者 | Yeh, Horng-ming; Liu, Ming-fei; Chang, Kuo-kuan; Liu, Shian-min; Chen, Chang-hung; | 書刊名 | Journal of the Formosan Medical Association |
卷 期 | 109:1 2010.01[民99.01] |
頁 次 | 頁85-88 |
分類號 | 415.69 |
關鍵詞 | Adult-onset Still's disease; Hemophagocytic syndromes; Jaundice; |
語 文 | 英文(English) |
英文摘要 | Hemophagocytic syndrome (HS) that occurs in the course of adult-onset Still's disease (AOSD) has been reported only rarely in the literature. HS and AOSD share overlapping clinical and laboratory features, therefore, it is difficult to recognize HS as a complication of AOSD. Here, we report the case of a 46-year-old woman with classical features of AOSD. Severe pancytopenia and jaundice associated with extreme hyperferritinemia occurred during high-dose steroid treatment. Bone marrow biopsy showed typical pathological features of hemophagocytosis, which confirmed the coexistence of HS with AOSD. The patient was treated with methylprednisolone pulse therapy of 500 mg/day for 3 days, as recommended in cases of HS complicating AOSD, and her condition improved gradually. During the disease course, extensive studies could not identify any viral infection or other known underlying etiology for the reactive hemophagocytosis. Currently, the patient is in remission on low-dose prednisolone and azathioprine. |
本系統中英文摘要資訊取自各篇刊載內容。